A Case of Thoracic Endovascular Aortic Repair for Subacute Aortic Dissection Stanford Type B in a Patient with Marfan Syndrome

Shun Nakaji*	Takashi Miura*	Ichiro Matsumaru*
Akihiko Tanigawa*	Yutaro Kawaguchi*	Shunsuke Taguchi*
Yugo Murakami*	Kikuko Obase*	Kiyoyuki Eishi*
Shinichiro Taniguchi**

(Department of Cardiovascular Surgery, Nagasaki University Hospital*, Nagasaki, Japan, and Department of Cardiovascular Surgery, Sasebo Chuo Hospital**, Sasebo, Japan).

A 41-years-old man with Marfan syndrome developed acute aortic dissection Stanford Type B. A new entry was located at the distal aortic arch. Medical treatment was given for a month, but the proximal descending aorta expanded to 50 mm. Because he had undergone partial arch replacement at the age of 36, thoracic endovascular aortic repair (TEVAR) using the synthetic graft as proximal landing zone was performed to close the entry. Six months after TEVAR, the false lumen around the stent graft disappeared. Distal stent graft-induced new entry (d-SINE) did not occur after TEVAR. Three years after TEVAR, we performed thoracoabdominal aortic replacement because of expansion of the residual false lumen without any complication. Endovascular therapy could be useful option for extensive aortic lesion even in Marfan syndrome.

 

Jpn. J. Cardiovasc. Surg. 51 : 48-52 (2022)

Keywords：Marfan syndrome ; aortic dissection ; endovascular therapy ; TEVAR