Left Subclavian Artery Aneurysm with von Recklinghausen’s Disease

Kyohei Ueno＊	Megumu Kanno＊	Hirofumi Midorikawa＊
Gaku Takinami＊	Ken Niitsuma＊

（Cardiovascular Surgery, Southern Tohoku General Hospital＊, Koriyama, Japan）

A 60-year-male patient complained of stomachache, for which he underwent a computed tomography scan. A 35-mm, saccular aneurysm was detected in the left subclavian artery. He was diagnosed with von Recklinghausen’s disease（vR disease）from the characteristic physical findings of numerous neurofibromatosis and Cafe´-au-lait spots, as well as intra-sibling onset. A median sternotomy was performed, and the subclavian arterial aneurysm was sacrificed. A bypass connection was established between the ascending aorta and the left axillary artery using the great saphenous vein, and all blood vessels that flowed into the aneurysm were ligated. Although vR disease is known to be associated with vascular lesions, isolated subclavian aneurysms are rare. Due to the low survival rate of ruptured aneurysms and the fragility of blood vessels in vR disease, it is important to make an early diagnosis and perform surgery.

 

Jpn. J. Cardiovasc. Surg. 50:420-424（2021）

Keywords：von Recklinghausen’s disease;subclavian artery;aorto-axillary artery bypass;coil embolization