Japanese Journal of Cardiovascular Surgery Vol47,No5

Staged Repair of Anomalous Origin of the Right Pulmonary Artery from the Ascending Aorta in a Low Birth Weight Infant:A Surgical Option for the Relief of the Postoperative Right Pulmonary Artery Stenosis
Takeshi Kawamata* Mio Noma* Tomomi Nakajima*
Muneaki Matsubara* Hideyuki Kato* Chiho Tokunaga*
Hiroaki Sakamoto* Yuji Hiramatsu*

(Department of Cardiovascular Surgery, University of Tsukuba Hospital*, Tsukuba, Japan)

A premature boy was born after 35 weeks gestation(1,561g in weight)with a diagnosis of anomalous origin of the right pulmonary artery from the ascending aorta(AORPA)and perimembranous ventricular septal defect(VSD). The fourteenth day after birth, banding of the right pulmonary artery was performed as a palliative operation. At the age of 5 months(3.9kg in weight), the right pulmonary artery branched from the ascending aorta, and was anastomosed to a flap made by the lateral wall of the main pulmonary artery with pericardial patch augmentation. VSD patch closure was performed concomitantly. Severe stenosis of the right pulmonary artery compressed by the ascending aorta and left pulmonary hypertension were revealed 3 weeks after the repair. At the age of 11 months, a surgical relief of the right pulmonary artery stenosis was performed. Transection of the ascending aorta provided an excellent exposure of the right posterior pulmonary artery. After patch plasty of the stenotic pulmonary artery, the divided ascending aorta was restored using a strip form patch on 4/5 circle of its posterior wall to extend the aorta and widen the space for the right pulmonary artery. This technique preserves growth potential of the ascending aorta. There are few reports of surgical repair of AORPA with VSD in low birth weight infants. We presented here a case with surgical relief of post-operative right pulmonary artery stenosis. Long term observation of repaired right pulmonary artery, and requiring residual slight hypertension of the left pulmonary artery.

 

Jpn. J. Cardiovasc. Surg. 47:207-210(2018)

Keywords:anomalous origin of the right pulmonary artery from the ascending aorta;low birth weight infant;staged repair;pulmonary artery reconstruction


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