A Surgical Case for Acute Heart Failure in a 1-month-old Infant with a Right Cervical Aortic Arch

(Department of Cardiovascular Surgery, Saitama Children’s Medical Center, Saitama, Japan)

Koji Nomura Takayuki Abe Yoshihiro Ko
A 2-day-old male baby was referred to our hospital because of a heart murmur. We diagnosed as a right cervical aortic arch, and coarctation between the right carotid and right subclavian artery. On echocardiography, the velocity at the coarctation was 1.8m/s, the left ventricular ejection fraction(LVEF)was 53%, and he was asymptomatic during the neonatal period. A chromosome examination showed a deletion of 22q11 syndrome. At 1 month, he weighted 3.8kg and was readmitted to our hospital for wheezing. Echocardiography showed a left ventricular dysfunction with LVEF of 24%. The coarctation velocity increased to 5.1m/s. An urgent operation was performed because of a severely depressed cardiac function. His LVEF increased to 67%, and the velocity was less than 1m/s postoperatively, and he was discharged on postoperative day 32. We report a rare neonatal surgical case of a right cervical arch with a coarctation.
  Jpn. J. Cardiovasc. Surg. 41:128-131(2012)

Keywords:right cervical aortic arch, 22q11 deletion, coarctation, ventricular dysfunction, infant