Aortic Root Replacement for Perivalvular Leakage after Aortic Valve Replacement for Marfan Syndrome with Severe Thoracic Deformity

(Department of Cardiovascular Surgery, Kinki University School of Medicine, Osakasayama, Japan)

Takako Nishino Toshihiko Saga Hitoshi Kitayama
Susumu Nakamoto Kiyoaki Takaba Kousuke Fujii
Shintaro Yukami
The number of operations performed for cardiovascular disease has increased since recent improvements in diagnostic and the therapeutic technology have led to a remarkable increase in the life expectancy of patients with Marfan syndrome. On the other hand, operative procedures can be difficult when patients have complications of connective tissue abnormalities such as thoracic deformities, lung diseases and ophthalmic lesions. Although recent surgical outcomes have improved, those of secondary surgery are more difficult. We describe aortic root replacement to treat perivalvular leakage after aortic valve replacement in a patient with Marfan syndrome with a severe thoracic deformity.
  Jpn. J. Cardiovasc. Surg. 40:14-18(2011)

Keywords:Marfan syndrome, perivalvular leakage, thoracic deformities, secondary surgery