A Ruptured Anterior Tibial Artery Aneurysm in a Patient with von Recklinghausen's Disease

(Department of Cardiovascular Surgery, Niigata City Hospital, Niigata, Japan)

Shuichi Shiraishi Kenji Aoki Hiroshi Amano
Yoshiki Takahashi Satoshi Nakazawa Hiroshi Kanazawa
A 41-year-old woman with neurofibromatosis (NF) was admitted to our hospital for severe pain and right leg swelling of 5days duration. Paralysis of the right leg due to compartment syndrome was also recognized. She had been diagnosed as von Recklinghausen's neurofibromatosis, previously. 3D-computed tomography showed a ruptured anterior tibial artery aneurysm. There was a normal patent posterior tibial artery. Since her complaint of pain was severe, we performed an emergency operation. Under the pneumatic tourniquet technique, the aneurysm was resected, and both the proximal and distal sides of the anterior tibial artery were ligated. A massive hematoma was completely removed. Postoperatively, the dorsalis pedis and posterior tibial pulses remained palpable. The paralysis improved considerably and she was given an ambulatory discharge from our hospital 21days after the operation. Histological examination revealed proliferating wavy spindle cells infiltrating between the adventitia and mesothelium of the aneurysmal wall and staining positively for S100 immunoperoxidase.
@Jpn. J. Cardiovasc. Surg. 35: 210-212 (2006)