| A Case of Marfan's Syndrome with
Acute Aortic Dissection during Pregnancy |
(Department of Cardiovascular Surgery, Jikei University
School of Medicine, Tokyo, Japan)
| Takahiro Inoue |
Yoshimasa Sakamoto |
Hiroshi Okuyama |
| Makoto Hanai |
Noriyasu Kawada |
Gen Shinohara |
| Kazuhiro Hashimoto |
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We present a case of Marfan's syndrome
with acute aortic dissection during the trimester of her pregnancy,
who underwent a Bentall operation 2 days after emergency cesarean
section. A 24-year-old woman during the 31st week of pregnancy
visited our emergency room due to sudden onset of chest and back
pain, though she had no abnormality until this event. Because
of her tall height, spider fingers, positive wrist sign, visual
disorder and scoliosis, she was given a diagnosis of Marfan's
syndrome. Enhanced CT and cardiac ultrasonography revealed that
she was suffering from acute aortic dissection with annulo-aortic
ectasia. Since it was difficult for her to continue with her
pregnancy, she underwent emergency cesarean section and gave
birth to a male baby weighted 1,706g. Although there was little
likelifood of early thrombus formation in the false lumen or
significant aortic regurgitation indicating an emergency operation,
fear of massive bleeding from her uterus and the exfoliated surface
of the placenta after cesarean section required an observation
period of 2 days. We performed a Bentall operation successfully
after careful sedation, ventilation and blood pressure control
for 2 days.
Jpn. J. Cardiovasc. Surg.34: 116-119 (2005) |
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