| A Case of Marfan's Syndrome with
Repeated Occurrence of Acute Aortic Dissection during Treatment |
| Shun-ichiro Sakamoto |
Masami Ochi |
Naoko Okubo |
| Yosuke Ishii |
Ryuzo Bessho |
Shigeo Tanaka |
(Department of Surgery II, Cardiovascular Surgery,
Nippon Medical School, Tokyo, Japan)
|
A 26-year-old man with Marfan's
syndrome suffered aortic dissection repeatedly during hospitalization.
He was admitted with a diagnosis of annuloaortic ectasia with
severe aortic regurgitation. A type A aortic dissection occurred
after diagnostic angiography. Three weeks after the onset of
the dissection, an aortic root replacement in combination with
a total arch replacement was performed. Eight months later, residual
dissection in the descending thoracic aorta was replaced with
distal perfusion by a temporary bypass from the left subclavian
artery to the descending thoracic aorta. At the termination of
the operation, abdominal aortic dissection occurred with acute
bilateral limb ischemia, which was treated with abdominal aortic
intimal fenestration. He recovered uneventfully and was discharged
3 weeks after operation. In light of our experience, because
of vascular fragility, great care should be taken in treating
patients with Marfan's syndrome to avoid iatrogenic aortic dissection.
Jpn. J. Cardiovasc. Surg. 31：282-284 (2002) |
|
