| A Case of Tetralogy of Fallot
with Endocardial Cushion Defect of the Intact Primary Septum |
| Shingo Ohuchi |
Takanori Oka |
Hajime Kin |
| Osamu Ohtsu |
Koutaro Oyama |
Hiroshi Izumoto |
| Kazuaki Ishihara |
Kohei Kawazoe |
|
(Iwate Medical University Memorial Heart Center,
Morioka, Japan)
|
The patient was a 15-month-old girl
with Down's syndrome. She had a heart murmur on the first day
after birth. The echocardiogram revealed that she had the tetralogy
of Fallot (TOF) and mitral insufficiency (MI). She was observed
because she had no heart failure or cyanosis. However, she developed
heart failure with progressive MI. Then, she was admitted to
our medical center for surgical treatment. During the operation,
it was confirmed that the primary septum was intact and a large
ventricular septal defect was located at the inlet to outlet
portion with anterior malalignment. Each leaflet of the atrioventricular
valve were attached to the same level and the ventricular septum
was scooped out. TOF with endocardial cushion defect (ECD) without
primary septal defect was diagnosed based on the operative findings.
Surgical repair was performed through the right atrium and pulmonary
artery. She was discharged 17 days after operation without any
complications. This was a very rare combination of TOF with ECD
without a primary septal defect. We discussed this rare condition
with a review of the literature.
Jpn. J. Cardiovasc. Surg. 31: 202-204（2002) |
|
