症例52

心底面の冠状溝に沿って線状の石灰化。

右肺門付近に4.5×3.0mm程度の結節状の石灰化

腹水あり。CT値は25程度と高く、血性の可能性あり。

左外腸骨静脈から下大静脈内にかけて、カテーテルの断面のような点状の高吸収あり。

• 参考文献） Pathologica. 2015 Mar;107(1):29-31. A rare cause of death in infancy: idiopathic infantile arterial calcification. Amine M, Faten H, Rim H, Nidhal HS, Njim L, Moussa A, Zakhama A. Abstract The aim of this paper is to report the autopsy findings of an Idiopathic Infantile Arterial Calcification-new-born male and describe its follow-up. Y.R, a 23-days-old male, hasn't any relevant personal past medical or family history. The baby was weighing 3.2 kg at birth. He was breast fed and appeared to be perfectly normal. In the last 24 hours, he presented to the family doctor with vomitis, refuse of feeds without fever or diarrhea. He was diagnosed as having gastroenteritis and was medicated accordingly. A few hours later, he had an hematemese episode associated with facial cyanosis. Death occurred despite cardio-pulmonary resuscitation. Forensic autopsy was required. The macroscopic examination showed a bilateral pleural liquid effusion without any other abnormalities. Microscopic investigation revealed a generalized arterial calcification of all organs. Idiopathic arterial calcification is primarily a disease of infancy. It is characterized pathologically by generalized arterial calcification within the internal elastic lamina, associated with intimal fibrous proliferation. Death occur often in the first sixth months due to heart failure.