{"id":9106,"date":"2016-07-03T15:12:26","date_gmt":"2016-07-03T06:12:26","guid":{"rendered":"\/sawamura\/?p=9106"},"modified":"2021-11-02T15:52:36","modified_gmt":"2021-11-02T06:52:36","slug":"diffuseleptomeningealglioneuronaltumor","status":"publish","type":"post","link":"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/diffuseleptomeningealglioneuronaltumor\/","title":{"rendered":"Diffuse leptomeningeal glioneuronal tumor  DLGNT"},"content":{"rendered":"<ul>\n<li>\u5c0f\u5150\u671f\u3068\u601d\u6625\u671f\u306b\u751f\u3058\u307e\u3059<\/li>\n<li><span style=\"color: #000080;\"><strong>\u3086\u3063\u304f\u308a\u5897\u5927\u3059\u308b\u816b\u760d<\/strong><\/span>\u3067\u3059<\/li>\n<li>disseminated oligodendroglial-like leptomengeal tumor\u3068\u547c\u3070\u308c\u307e\u3057\u305f<\/li>\n<li>\u3053\u306e\u540d\u306e\u793a\u3059\u3088\u3046\u306a\u7279\u5fb4\u3092\u793a\u3057\u307e\u3059<\/li>\n<li><span style=\"color: #000080;\"><strong>\u8133\u810a\u9ac4\u819c leptomeninges\u306b\u5e83\u7bc4\u56f2\u306b\u3073\u307e\u3093\u6027\u306b\u5b58\u5728<\/strong><\/span>\u3057\u307e\u3059<\/li>\n<li>\u3064\u307e\u308a\uff0c\u304f\u3082\u819c\u4e0b\u8154\u3068\u8133\u5ba4\u3092\u6e80\u305f\u3059\u3088\u3046\u306b\u5897\u6b96\u3057\u307e\u3059<\/li>\n<li>\u8133\u810a\u9ac4\u306e\u9ac4\u819c\u306b\u7121\u6570\u306e\u7d50\u7bc0\u304c\u3067\u304d\uff0c\u8133\u810a\u9ac4\u306e\u8868\u9762\u304c\u30ac\u30c9\u30ea\u30cb\u30a6\u30e0\u5897\u5f37\u3055\u308c\u307e\u3059<\/li>\n<li>MRI\u3067\u306f\u60aa\u6027\u816b\u760d\u306e\u64ad\u7a2e\u3067\u3042\u308b\u3068\u8a3a\u65ad\u3055\u308c\u307e\u3059<\/li>\n<li>\u5e83\u304c\u308a\u3068\u3057\u3066\u306f\uff0c\u6bcd\u6591\u75c7\u3067\u3042\u308bmeningeal melanomatosis\u306b\u4f3c\u3066\u3044\u307e\u3059<\/li>\n<li>\u810a\u9ac4\u3067\u306f\u9ac4\u5185\u3067\u816b\u7624\u3092\u4f5c\u308a\u307e\u3059<\/li>\n<li>\u305d\u306e\u305f\u3081\u306b\u9ac4\u6db2\u5438\u53ce\u3042\u308b\u3044\u306f\u9589\u585e\u6027\u306e\u96e3\u6cbb\u6027\u6c34\u982d\u75c7\u3068\u306a\u308a\u307e\u3059<\/li>\n<li><span style=\"color: #000080;\"><strong>\u4e88\u5f8c\u4e0d\u826f<\/strong><\/span>\u3067\u3059<\/li>\n<li>\u4e4f\u7a81\u8d77\u81a0\u816b\u306b\u898b\u3089\u308c\u308b\u3088\u3046\u306a\uff0cmonomorphic clear cell glial morphology\u3092\u5448\u3057\u307e\u3059<\/li>\n<li>\u514d\u75ab\u67d3\u8272\u3067\u306f\uff0cOLIG 2, S-100\u306b\u52a0\u3048\u3066 synaptophysin\u304c\u967d\u6027\u3068\u306a\u308b\u305f\u3081\u306b\uff0cglioneuronal\u3068\u8868\u73fe\u3055\u308c\u307e\u3059<\/li>\n<li>1p deletion\u3082\u3057\u304f\u306f<em>BRAF<\/em> fusion\u304c\u3042\u308a\uff0c\u307e\u308c\u306b19q deletion\u304c\u307f\u3089\u308c\u307e\u3059<\/li>\n<li>IDH mutation\u306f\u3042\u308a\u307e\u305b\u3093<\/li>\n<li>MIB-1\u67d3\u8272\u7387\u304c\u9ad8\u304f\uff0c\u5897\u5927\u901f\u5ea6\u306f\u901f\u3044\u3082\u306e\u3067\u306f\uff0c\u4e88\u5f8c\u4e0d\u826f\u3067\u3059<\/li>\n<li>\u6cbb\u7642\u65b9\u6cd5\u306f\u77e5\u3089\u308c\u3066\u3044\u307e\u305b\u3093<\/li>\n<li>\u904e\u8aa4\u816b\u3042\u308b\u3044\u306f\u5f62\u6210\u4e0d\u5168\u3068\u3082\u3044\u3048\u308b\u816b\u760d\u3067\u3059<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>\u5c0f\u5150\u671f\u3068\u601d\u6625\u671f\u306b\u751f\u3058\u307e\u3059 \u3086\u3063\u304f\u308a\u5897\u5927\u3059\u308b\u816b\u760d\u3067\u3059 disseminated oligodendroglial-like leptomengeal tumor\u3068\u547c\u3070\u308c\u307e\u3057\u305f \u3053\u306e\u540d\u306e\u793a\u3059\u3088\u3046\u306a\u7279\u5fb4\u3092\u793a\u3057\u307e\u3059 \u8133\u810a\u9ac4\u819c l 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