{"id":6289,"date":"2014-10-24T15:51:16","date_gmt":"2014-10-24T06:51:16","guid":{"rendered":"\/sawamura\/?p=6289"},"modified":"2025-09-09T11:08:20","modified_gmt":"2025-09-09T02:08:20","slug":"hamartomas","status":"publish","type":"post","link":"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/hamartomas\/","title":{"rendered":"\u3066\u3093\u304b\u3093\u3092\u751f\u3058\u3084\u3059\u3044\u826f\u6027\u816b\u760d\u3000hamartoma\uff0cglioneuronal and neuronal tumors\uff0c\u5c0f\u5150\u306e\u4f4e\u60aa\u6027\u5ea6\u30b0\u30ea\u30aa\u30fc\u30de"},"content":{"rendered":"<h5>glioneuronal and neuronal tumors<\/h5>\n<h5>\u3066\u3093\u304b\u3093\u306e\u539f\u56e0\u3068\u306a\u308b WHO \u30b0\u30ec\u30fc\u30c91 \u306e\u826f\u6027\u816b\u760d\u306e\u7fa4\u3067\u3059<\/h5>\n<h5>\u75c5\u7406\u78ba\u5b9a\u8a3a\u65ad\u304c\u3064\u304b\u305a\uff0c\u904e\u8aa4\u816b hamartoma \u76ae\u8cea\u5f62\u6210\u7570\u5e38 cortical dysplasia \u3068\u3055\u308c\u308b\u3082\u306e\u3082\u591a\u3044\u3067\u3059<\/h5>\n<h5 align=\"left\"><strong>WHO 2021\u5e74\u5206\u985e\u306e\uff0c\u30b0\u30ea\u30a2\u795e\u7d4c<\/strong><strong>\u7d30\u80de\u3068\u795e\u7d4c\u7d30\u80de\u3092\u8d77\u6e90\u3068\u3059\u308b\u816b\u760d &#8216;<\/strong><strong>Glioneuronal and neuronal tumors&#8217; \u306e\u591a\u304f\u304c\u3053\u306e\u3088\u3046\u306a\u816b\u760d\u6027\u683c\u3092\u6709\u3057\u307e\u3059<\/strong><\/h5>\n<h4><span style=\"color: #000000;\">\u4f55\u304c\u904e\u8aa4\u816b\u3060\u3068\u8a00\u308f\u308c\u308b\u3068\u56f0\u308b\u3053\u3068\u3082\u3042\u308a\u307e\u3059\u304c\u4ee5\u4e0b\u306e\u3088\u3046\u306a\u3082\u306e\u3067\u3059<\/span><\/h4>\n<ul>\n<li><span style=\"color: #000080;\"><strong>\u8996\u5e8a\u4e0b\u90e8\u904e\u8aa4\u816b<\/strong><\/span>\u304c\u3082\u3063\u3068\u3082\u6709\u540d\u306a\u816b\u760d\u3067\u3059<\/li>\n<li><span style=\"color: #000080;\"><strong>\u795e\u7d4c\u7bc0\u81a0\u816b\u30b0\u30ec\u30fc\u30c9\uff11<\/strong><\/span>\u3082\u904e\u8aa4\u816b\u306b\u8fd1\u3044\u3082\u306e\u3067\u3059<\/li>\n<li>\u795e\u7d4c\u7bc0\u81a0\u816b\u306f\uff0cmixed neuronal glial tumor\u3068\u3082\u8a00\u308f\u308c\u307e\u3059<\/li>\n<li><span style=\"color: #000080;\"><strong>\u30a2\u30f3\u30b8\u30aa\u30bb\u30f3\u30c8\u30ea\u30c3\u30af\u30fb\u30b0\u30ea\u30aa\u30fc\u30de \u8840\u7ba1\u4e2d\u5fc3\u6027\u81a0\u816b angiocentric glioma<\/strong><\/span><\/li>\n<li><span style=\"color: #000080;\"><strong>\u7b2c4\u8133\u5ba4\u5e8a\u904e\u8aa4\u816b<\/strong><\/span><\/li>\n<li><span style=\"color: #000080;\"><strong>Polymorphous low-grade neuroepithelial tumor of the young<\/strong><\/span><\/li>\n<li><span style=\"color: #000080;\"><strong>Multinodular and vacuolating neuronal tumor<\/strong><\/span><\/li>\n<li><span style=\"color: #000080;\"><b>Diffuse low-grade glioma, MAPK pathway-altered<\/b><\/span><\/li>\n<li>\u4ed6\u306e\u3082\u308d\u3082\u308d\u306e\u795e\u7d4c\u81a0\u7d30\u80de\u816b\u760d neuronal glial tumors\u3042\u308b\u3044\u306f<span style=\"color: #000080;\"><strong>\u904e\u8aa4\u816b\u69d8\u795e\u7d4c\u81a0\u7d30\u80de\u816b\u760dhamartomatous glial neuronal tumors<\/strong><\/span>\u3068\u547c\u3070\u308c\u308b\u3082\u306e\u306f\u305f\u304f\u3055\u3093\u3042\u308a\u307e\u3059<\/li>\n<li>\u75c5\u7406\u7d44\u7e54\u3092\u307f\u3066\u3082\u78ba\u5b9a\u8a3a\u65ad\u540d\u304c\u3064\u304b\u306a\u3044\u3088\u3046\u306a\u3082\u306e\u3082\u591a\u3044\u3067\u3059<\/li>\n<\/ul>\n<h4><span style=\"color: #000000;\">\u5927\u307e\u304b\u306a\u3053\u3068<\/span><\/h4>\n<ul>\n<li>\u816b\u760d\u3067\u306f\u306a\u304f\u3066\u8133\u7d44\u7e54\u306e\u5f62\u6210\u7570\u5e38\u306b\u8fd1\u3044\u3082\u306e\u3067\u3059<\/li>\n<li>\u8133\u306e\u7d30\u80de\uff08\u795e\u7d4c\u7d30\u80de\u3068\u30b0\u30ea\u30a2\u7d30\u80de\u30fb\u795e\u7d4c\u81a0\u7d30\u80de\uff09\u304c\u307e\u3061\u304c\u3063\u3066\u5897\u3048\u3059\u304e\u3066\u3057\u307e\u3063\u305f\u75c5\u5909\u3067\u3059<\/li>\n<li>\u3067\u3059\u304b\u3089\uff0c\u751f\u307e\u308c\u3064\u304d\uff0c\u5e7c\u5c0f\u5150\u306b\u591a\u3044\u3082\u306e\u3067\u3059<\/li>\n<li>\u771f\u306e\u816b\u760d\uff08\u65b0\u751f\u7269 neoplasm\uff09\u3067\u306f\u306a\u3044\u306e\u3067\u5927\u304d\u304f\u306a\u308a\u307e\u305b\u3093<\/li>\n<li>\u5076\u7136\u767a\u898b\u3055\u308c\u308b\u3053\u3068\u304c\u591a\u3044\u3067\u3059<\/li>\n<li>\u75c7\u72b6\u306e\u306a\u3044\u3082\u306e\u306f\u753b\u50cf\u8a3a\u65ad\u3060\u3051\u3067\u3001\u4f55\u3082\u3057\u306a\u3044\u3067\u307b\u3063\u3066\u304a\u304d\u307e\u3059<\/li>\n<li>\u75c7\u72b6\u3092\u51fa\u3059\u3068\u3059\u308c\u3070\uff0c\u307b\u3068\u3093\u3069\u304c<strong><span style=\"color: #ff0000;\">\u3066\u3093\u304b\u3093\u767a\u4f5c<\/span><\/strong>\u3067\u3059<\/li>\n<li>\u5927\u8133\u8868\u9762\uff08\u7070\u767d\u8cea\uff09\u306b\u8fd1\u3044\u6240\u306b\u3067\u304d\u307e\u3059<\/li>\n<li>\u6458\u51fa\u3059\u308b\u3068\u3066\u3093\u304b\u3093\u767a\u4f5c\u304c\u6e1b\u3063\u305f\u308a\u7121\u304f\u306a\u3063\u305f\u308a\u3059\u308b\u3053\u3068\u3082\u3042\u308a\u307e\u3059<\/li>\n<\/ul>\n<h5><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u8996\u5e8a\u4e0b\u90e8\u904e\u8aa4\u816b hypothalamic hamartoma\" href=\"\/sawamura\/pediattumor\/hamartoma\/\">\u8996\u5e8a\u4e0b\u90e8\u904e<\/a><a style=\"color: #000080;\" title=\"\u8996\u5e8a\u4e0b\u90e8\u904e\u8aa4\u816b hypothalamic hamartoma\" href=\"\/sawamura\/pediattumor\/hamartoma\/\">\u8aa4\u816b\uff08\u3053\u3053\u3092\u30af\u30ea\u30c3\u30af\u3059\u308b\u3068\u307f\u308c\u307e\u3059\uff09<\/a><\/strong><\/span><\/h5>\n<h5><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u795e\u7d4c\u7bc0\u7d30\u80de\u816b\uff0c\u795e\u7d4c\u7bc0\u81a0\u816b\" href=\"\/sawamura\/braintumors\/glioma\/gangliocyto\/\">\u795e\u7d4c\u7bc0\u81a0\u816b\u30b0\u30ec\u30fc\u30c9<\/a><a style=\"color: #000080;\" title=\"\u795e\u7d4c\u7bc0\u7d30\u80de\u816b\uff0c\u795e\u7d4c\u7bc0\u81a0\u816b\" href=\"\/sawamura\/braintumors\/glioma\/gangliocyto\/\">\uff11\uff08\u3053\u3053\u3092\u30af\u30ea\u30c3\u30af\u3059\u308b\u3068\u307f\u308c\u307e\u3059\uff09<\/a><\/strong><\/span><\/h5>\n<hr \/>\n<h5><span style=\"color: #000080;\">Angiocentric glioma\u00a0<\/span><span style=\"color: #000080; font-size: 1.2em;\">WHO grade 1<br \/>\n<\/span><span style=\"color: #000080;\">\u30a2\u30f3\u30b8\u30aa\u30bb\u30f3\u30c8\u30ea\u30c3\u30af\u30fb\u30b0\u30ea\u30aa\u30fc\u30de<\/span><\/h5>\n<p><strong>\u3073\u307e\u3093\u6027\u661f\u7d30\u80de\u816b,\u00a0<em>MYB<\/em>\u3042\u308b\u3044\u306f<em>MYBL1\u00a0<\/em>\u907a\u4f1d\u5b50\u7570\u5e38\u00a0\u00a0(\u30b0\u30ec\u30fc\u30c91)<\/strong><br \/>\n<strong>Diffuse astrocytoma, <em>MYB<\/em> or <em>MYBL1<\/em>-altered<\/strong><\/p>\n<h4>\u81e8\u5e8a\u6240\u898b<\/h4>\n<ul>\n<li>\u8840\u7ba1\u4e2d\u5fc3\u6027\u81a0\u816b\u3068\u3067\u3082\u8a33\u3059\u306e\u3067\u3059\u304c\uff0c\u65e5\u672c\u8a9e\u306f\u4f7f\u308f\u308c\u307e\u305b\u3093<\/li>\n<li>2021\u5e74\u304b\u3089\u540d\u79f0\u304c\u5909\u308f\u308a\uff0c\u5c0f\u5150\u306e\u5b9a\u60aa\u5236\u5ea6\u3073\u307e\u3093\u6027\u661f\u7d30\u80de\u816b\u306b\u5206\u985e\u3055\u308c\u307e\u3059<\/li>\n<li><span style=\"color: #000080;\"><strong>MYB\u3042\u308b\u3044\u306fMYBL1\u907a\u4f1d\u5b50\u306e\u7570\u5e38<\/strong><\/span>\u3092\u3082\u3061\uff0c\u3073\u307e\u3093\u6027\u6d78\u6f64\u3092\u793a\u3059\u661f\u7d30\u80de\u6027\u816b\u760d\u3067\u3059<\/li>\n<li>\u5358\u8abf\u306a\u816b\u760d\u7d30\u80de\u304b\u3089\u69cb\u6210\u3055\u308c\u308b\u4f4e\u60aa\u6027\u5ea6\u816b\u760d\u3067\u3042\u308b<\/li>\n<li>\u75c7\u5019\u6027\u3066\u3093\u304b\u3093\uff08\u3051\u3044\u308c\u3093\u767a\u4f5c\uff09\b\u3092\u751f\u3058\u307e\u3059<\/li>\n<li><span style=\"color: #000080;\"><strong>\u4f55\u5e74\u306b\u3082\u308f\u305f\u3063\u3066\u90e8\u5206\u767a\u4f5c\u3092\u751f\u3058\u3066\u6162\u6027\u5316\u3042\u308b\u3044\u306f\u96e3\u6cbb\u5316\u3059\u308b\u3066\u3093\u304b\u3093\u767a\u4f5c<\/strong><\/span>\u304c\u591a\u3044\u3067\u3059<\/li>\n<li>\u5c0f\u5150\u671f\u3068\u82e5\u5e74\u6210\u4eba\u3067\u767a\u75c7\u3057\u307e\u3059<\/li>\n<li><strong><span style=\"color: #000080;\">\u5e74\u9f62\u4e2d\u592e\u5024\u306717\u624d<\/span><\/strong>\u304f\u3089\u3044\u3067\u3059<\/li>\n<li>\u7121\u75c7\u72b6\u3067\u5076\u7136\u767a\u898b\u3055\u308c\u308b\u3082\u306e\u304c\u591a\u3044\u3067\u3059<\/li>\n<li>\u524d\u982d\u982d\u9802\u8449\uff0c\u5074\u982d\u8449\u3001\u6d77\u99ac\u3068\u6d77\u99ac\u508d\u56de\uff0c\u982d\u9802\u8449\u306e\u9806\u306b\u591a\u3044\u3067\u3059<\/li>\n<li>\u753b\u50cf\u521d\u898b\u306f\uff0c<strong><span style=\"color: #000080;\">\u795e\u7d4c\u81a0\u816b\u30b0\u30ec\u30fc\u30c91\u3084DNT\u306b\u4f3c\u3066\u3044\u307e\u3059<\/span><\/strong><\/li>\n<li><strong><span style=\"color: #000080;\">\u5927\u8133\u8868\u5728\u6027\u306e\u816b\u760d<\/span><\/strong>\u3067\uff0c\u7070\u767d\u8cea\u3092\u4fb5\u3059\u75c5\u5909\u3067\u3059<\/li>\n<li>\u5883\u754c\u306f\u660e\u77ad\u3067\u3059\u304c\uff0c\u5468\u56f2\u304c\u3054\u304f\u4e00\u90e8\u306b\u3058\u3080\u3088\u3046\u306a\u6240\u3082\u3042\u308a\u307e\u3059<\/li>\n<li>T2\/FLAIR\u753b\u50cf\u3067\u9ad8\u4fe1\u53f7\u3068\u306a\u308a\u307e\u3059<\/li>\n<li><strong><span style=\"color: #000080;\">\u8133\u8cea\u58c1\u306b\u5411\u304b\u3063\u3066\u67c4\uff08\u830e stalk)\u306e\u3088\u3046\u306a\u75c5\u5909\u304c\u7d9a\u304f<\/span><\/strong> stalk-like extension \u306e\u304c\u7279\u5fb4\u3068\u3055\u308c\u3066\u3044\u307e\u3059\u304c\uff0c\u305d\u308c\u304c\u898b\u3089\u308c\u306a\u3044\u3082\u306e\u3082\u591a\u3044\u3067\u3059\u3057\uff0c\u76ae\u8cea\u7570\u5f62\u6210\u3067\u3082\u3053\u306e\u6240\u898b\u3092\u6301\u3064\u3082\u306e\u304c\u3042\u308a\u307e\u3059<\/li>\n<li>\u753b\u50cf\u8a3a\u65ad\u3067angiocentric glioma\u3092\u7591\u3063\u305f\u3089MRI\u3067\u7d4c\u904e\u89b3\u5bdf\u3057\u307e\u3059<\/li>\n<li>\u5927\u304d\u304f\u306a\u3089\u306a\u3044\u306e\u3067\u624b\u8853\u6458\u51fa\u306a\u3069\u306e\u6cbb\u7642\u306e\u5fc5\u8981\u306f\u3042\u308a\u307e\u305b\u3093<\/li>\n<li>\u3066\u3093\u304b\u3093\u304c\u91cd\u304f\u306a\u3063\u3066\u85ac\u3067\u30b3\u30f3\u30c8\u30ed\u30fc\u30eb\u304c\u96e3\u3057\u3044\u6642\u306b\u306f\u958b\u982d\u624b\u8853\u3067\u306e\u6458\u51fa\u3092\u8003\u3048\u307e\u3059<\/li>\n<\/ul>\n<h4>\u75c5\u7406<\/h4>\n<ul>\n<li>\u69cb\u6210\u7d30\u80de\u306f\uff0c\u816b\u760d\u5316\u3057\u305f\u6d78\u6f64\u6027\u306e\u661f\u7d30\u80de\u3068\u4e0a\u8863\u7d30\u80de\u5206\u5316\u3067\u3059<\/li>\n<li>\u76ae\u8cea\u8840\u7ba1\u306e\u5468\u56f2\u306b\u4e21\u6975\u6027\u306e\u816b\u760d\u7d30\u80de monomorphous bipolar cells \u304c\u914d\u5217\u3057\u307e\u3059<\/li>\n<li>\u6bdb\u69d8\u7d30\u80de\u6027\u661f\u7d30\u80de\u816b\u306e\u3088\u3046\u306b\uff0cangiocentric pattern\u3092\u3068\u308b\u3053\u3068\u304b\u3089\u540d\u4ed8\u3051\u3089\u308c\u307e\u3057\u305f<\/li>\n<li>\u8840\u7ba1\u5468\u56f2\u306b\u816b\u760d\u7d30\u80de\u304c\u914d\u5217\u3057\u3066 peudorosettes\uff0c\u4e0a\u8863\u816b\u306e\u69cb\u9020\u306b\u985e\u4f3c\u3057\u307e\u3059\u304c\u4e0a\u8863\u816b\u3067\u306f\u3042\u308a\u307e\u305b\u3093<\/li>\n<li>GFAP, EMA\u304c\u967d\u6027\u3068\u306a\u308a\u307e\u3059<\/li>\n<li>\u58ca\u6b7b\u3084\u6838\u5206\u88c2\u50cf\u306f\u306a\u304f\uff0cMIB-1\u67d3\u8272\u7387\u306f1%\u4ee5\u4e0b\u3067\u3059<\/li>\n<li><em>MYB-QKI<\/em>\u00a0gene fusions\u304c\u539f\u56e0\u3067\u767a\u751f\u3057\u307e\u3059<\/li>\n<\/ul>\n<div>\n<h4><a href=\"http:\/\/www.pathologyoutlines.com\/topic\/cnstumorangiocentricglioma.html\">anglicentric glioma\u306e\u753b\u50cf\u306f\u4e0b\u306e\u30da\u30fc\u30b8\u3092\u53c2\u7167\u3057\u3066\u4e0b\u3055\u3044<\/a><\/h4>\n<p><a href=\"http:\/\/www.pathologyoutlines.com\/topic\/cnstumorangiocentricglioma.html\">http:\/\/www.pathologyoutlines.com\/topic\/cnstumorangiocentricglioma.html<\/a><\/p>\n<\/div>\n<hr \/>\n<h5><span style=\"color: #000080;\">Polymorphous low-grade neuroepithelial tumor of the young<br \/>\nWHO grade 1<br \/>\n<\/span><span style=\"color: #000080;\">PLNTY<\/span><\/h5>\n<ul>\n<li>2021\u5e74\u306eWHO\u5206\u985e\u3067\u8ffd\u52a0\u3055\u308c\u305f\u816b\u760d\u540d\u3067\u3059<\/li>\n<li>\u5f93\u6765\uff0chamartomatous neuronal-glial tumor\u3068\u8a3a\u65ad\u3055\u308c\u3066\u6765\u305f\u3082\u306e\u306e\u4e00\u90e8\u3067\u3059<\/li>\n<li>WHO\u30b0\u30ec\u30fc\u30c91\u306e\u3068\u3066\u3082\u304a\u3068\u306a\u3057\u3044\u816b\u760d\u3067\uff0c\u5897\u5927\u50be\u5411\u3092\u793a\u3057\u307e\u305b\u3093<\/li>\n<li>\u5074\u982d\u8449\u8868\u9762\u306b\u591a\u304f\u898b\u3089\u308c\u307e\u3059<\/li>\n<li>\u3066\u3093\u304b\u3093\u6e90\u6027\u304c\u5f37\u3044\uff0c<span style=\"color: #ff0000;\"><strong>\u96e3\u6cbb\u6027\u3066\u3093\u304b\u3093\u3092\u751f\u3058\u308b<\/strong><\/span>\u3068\u3057\u3066\u5831\u544a\u3055\u308c\u3066\u6765\u305f\u826f\u6027\u816b\u760d\u3067\u3059<\/li>\n<li>\u5c0f\u5150\u304b\u3089\u82e5\u5e74\u6210\u4eba\u306b\u767a\u751f\u3057\uff0c\u521d\u767a\u75c7\u72b6\u306f\u75c7\u5019\u6027\u3066\u3093\u304b\u3093 SLRE \u3067\u3059<\/li>\n<li>\u753b\u50cf\u3068\u75c5\u7406\u6240\u898b\u306f\uff0c\u4e4f\u7a81\u8d77\u81a0\u816b\u306b\u4f3c\u3066\u3044\u307e\u3059<\/li>\n<li>\u65e5\u672c\u8a9e\u8a33\u306f\u96e3\u3057\u3044\u3067\u3059\uff0c\u82e5\u5e74\u6027\u591a\u578b\u6027\u4f4e\u60aa\u6027\u5ea6\u795e\u7d4c\u4e0a\u76ae\u816b\u760d\u3068\u306a\u308a\u307e\u3059\u304c\u8a33\u304c\u308f\u304b\u308a\u307e\u305b\u3093<\/li>\n<li>\u5927\u8133\u8868\u9762\u306b\u591a\u304f\uff0cmass effect\u3092\u793a\u3055\u305a\u306b\u6d78\u6f64\u6027\u306b\u5897\u6b96\u3059\u308b \u3092\u542b\u3080\u30b0\u30ea\u30aa\u30fc\u30de\u306b\u898b\u3048\u307e\u3059<\/li>\n<li>\u753b\u50cf\u3067\u306f\uff0c<span style=\"color: #000080;\"><strong>\u7802\u7c92\u72b6\u77f3\u7070\u5316 grit carcification<\/strong><\/span>\u304c\u7279\u5fb4\u3067\uff0c\u306e\u3046\u80de\u5f62\u6210\u3059\u308b\u3053\u3068\u3082\u3042\u308a\uff0cFLAIR\u3067\u6ef2\u3080\u3088\u3046\u306b\u767d\u304f\u898b\u3048\u308b\u306e\u304c\u7279\u5fb4\u3067\u3059<\/li>\n<li>\u753b\u50cf\u3067\u306f\uff0c<strong><span style=\"color: #000080;\">T2\u5f37\u8abf\u753b\u50cf\u3067\u307e\u3060\u3089\u306a\u9ad8\u4fe1\u53f7<\/span> salt and pepper sign<\/strong>\uff0c\u30ac\u30c9\u30ea\u30cb\u30a6\u30e0\u3067\u90e8\u5206\u7684\u306b\u5897\u5f37\u3055\u308c\uff0c\u5883\u754c\u304c\u4e0d\u660e\u77ad\u3067\u67d3\u307f\u8fbc\u3080\u3088\u3046\u306b\u5e83\u304c\u3063\u3066\u3044\u307e\u3059<\/li>\n<li>WHO\u306e\u8a18\u8f09\u3059\u308b\u75c5\u7406\u50cf\u306f\u96d1\u591a\u306a\u6240\u898b\u3092\u542b\u307f\u307e\u3059\u304c\uff0c1) \u795e\u7d4c\u30b0\u30ea\u30a2\u7cfb\u816b\u760d\u3067\u3042\u308b\uff0c2) \u3073\u307e\u3093\u6027\u5897\u6b96\u50cf\u3092\u793a\u3059\uff0c3) \u4e4f\u7a81\u8d77\u81a0\u816b\u69d8\u306e\u7d44\u7e54\u50cf\u3092\u542b\u3080\uff0c4) \u77f3\u7070\u5316\u304c\u3042\u308b\uff0c5) <span style=\"color: #000080;\"><strong>CD34\u514d\u75ab\u67d3\u8272\u3067\u5f37\u967d\u6027<\/strong><\/span>\u3068\u306a\u308b\uff0c6) \u7d30\u80de\u6838\u3084\u7d30\u80de\u8cea\u306e\u5927\u5c0f\u4e0d\u540c\u304c\u3042\u308b polymorphous\uff0c7) MARK pathway\u6d3b\u6027\u5316\u3092\u793a\u3059\u907a\u4f1d\u5b50\u7570\u5e38\u304c\u3042\u308b\uff0c\u3068\u3055\u308c\u3066\u3044\u307e\u3059<\/li>\n<li>\u753b\u50cf\u306f\uff0c<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/32252664\/\">https:\/\/pubmed.ncbi.nlm.nih.gov\/32252664\/<\/a> \u3092\u53c2\u8003\u306b\u3057\u3066\u304f\u3060\u3055\u3044\u3002<\/li>\n<li class=\"heading-title\"><span class=\"authors-list-item \">Huse JT:\u00a0<\/span>Polymorphous low-grade neuroepithelial tumor of the young (PLNTY): an epileptogenic neoplasm with oligodendroglioma-like components, aberrant CD34 expression, and genetic alterations involving the MAP kinase pathway. Acta Neuropathol 2017<\/li>\n<li>Chen Y: Polymorphous low-grade neuroepithelial tumor of the young: case report and review focus on the radiological features and genetic alterations. BMC Neuro 2020<\/li>\n<\/ul>\n<hr \/>\n<h5><strong>\u591a\u7d50\u7bc0\u7a7a\u80de\u72b6\u795e\u7d4c\u7d30\u80de\u816b\u760d<br \/>\nMultinodular and vacuolating neuronal tumor MVNT<\/strong><\/h5>\n<ul>\n<li>\u5927\u8133\u8868\u9762\u306b\u8fd1\u3044\u76ae\u9ac4\u5883\u754c\u90e8\u306b\u898b\u3089\u308c\u308b\u816b\u760d\u3067\u3059<\/li>\n<li>\u591a\u304f\u306f\u7121\u75c7\u72b6\u3067\u5076\u7136\u767a\u898b\u3055\u308c\uff0c\u3073\u307e\u3093\u6027\u30b0\u30ea\u30aa\u30fc\u30de\u306e\u3088\u3046\u306b\u307f\u3048\u307e\u3059<\/li>\n<li>\u816b\u760d\u3068\u3057\u3066\u306f\u307b\u3068\u3093\u3069\u5927\u304d\u304f\u306a\u308a\u307e\u305b\u3093\u306e\u3067\uff0c\u7d4c\u904e\u89b3\u5bdf\u3057\u3066\u3082\u5909\u5316\u304c\u3042\u308a\u307e\u305b\u3093<\/li>\n<li>\u307e\u308c\u306b\u75c7\u5019\u6027\u3068\u306a\u308a\uff0c\u3066\u3093\u304b\u3093\u767a\u4f5c\u3092\u751f\u3058\u307e\u3059\uff08\u75c7\u5019\u6027\u3066\u3093\u304b\u3093\uff09<\/li>\n<li>MRI\u3067\u306f\uff0cT2\/FLAIR\u3067\u3073\u307e\u3093\u6027\u816b\u760d\u3068\u7d50\u7bc0\u72b6\u306e\u9ad8\u4fe1\u53f7\u304c\u6563\u5728\u3059\u308b\u3088\u3046\u306a\u7279\u6709\u306e\u753b\u50cf\u3092\u5448\u3057\u307e\u3059<\/li>\n<li>mass effect\u304c\u306a\u304f\u3066\uff0cT1\u4f4e\u4fe1\u53f7\uff0c\u30ac\u30c9\u30ea\u30cb\u30a6\u30e0\u5897\u5f37\u3055\u308c\u306a\u3044\u3073\u307e\u3093\u6027\u816b\u760d\u3067\u3059<\/li>\n<li>\u7a7a\u80de\u72b6\u306e\u795e\u7d4c\u7d30\u80de\u3068neuropil\u3067\u5f62\u6210\u3055\u308c\u307e\u3059\uff0c\u7d30\u80de\u5bc6\u5ea6\u306f\u758e\u3067\uff0c\u7d44\u7e54\u69cb\u7bc9\u306f\u7d50\u7bc0\u6027\u3067\u3059<\/li>\n<\/ul>\n<div class=\"page\" title=\"Page 1\">\n<div class=\"section\">\n<div class=\"layoutArea\">\n<div class=\"column\">\n<p>Turan A: <a href=\"http:\/\/www.turkishneurosurgery.org.tr\/pdf\/pdf_JTN_2529.pdf\">Advanced Magnetic Resonance Imaging Findings of Multinodular and Vacuolating Neuronal Tumor.<\/a> Turk Neurosurg 2021\uff08\u753b\u50cf\u53c2\u7167\u3067\u304d\u307e\u3059\uff09<\/p>\n<h5><span style=\"color: #000080;\"><b>Diffuse low-grade glioma, MAPK pathway-altered<\/b><\/span><\/h5>\n<ul>\n<li>\u5c0f\u5150\u306e\u5927\u8133\u534a\u7403\uff0c\u8133\u5e79\u90e8\uff0c\u5c0f\u8133\u306b\u767a\u751f\u3059\u308b\u816b\u760d\u3067\u3068\u3066\u3082\u3086\u3063\u304f\u308a\u5897\u5927\u3057\u307e\u3059<\/li>\n<li>\u753b\u50cf\u8a3a\u65ad\u3084\u75c5\u7406\u7d44\u7e54\u8a3a\u65ad\u3067\u306f\uff0c<span style=\"color: #000080;\"><strong>\u3073\u307e\u3093\u6027\u661f\u7d30\u80de\u816b\u3084\u4e4f\u7a81\u8d77\u81a0\u816b\u3068\u533a\u5225\u304c\u3064\u304d\u307e\u305b\u3093<\/strong><\/span><\/li>\n<li>IDH\u3084histon H3\u306b\u5909\u7570\u304c\u306a\u3044\u3053\u3068\u3067\u9451\u5225\u3067\u304d\u307e\u3059<\/li>\n<li>\u4ee3\u308f\u308a\u306b\uff0cMAP kinase pathway\u00a0(<i>BRAF, FGFR1, FGFR2, NTRK1, NTRK2, NTRK3, MAP2K1, MET<\/i> alterations) \u306b\u95a2\u308f\u308b\u907a\u4f1d\u5b50\u306b\u7570\u5e38\u304c\u8a8d\u3081\u3089\u308c\u307e\u3059<\/li>\n<li>\u7279\u306b\uff0cFGFR1\u3084BRAF\u306a\u3069\u3067\u3059<\/li>\n<li>\u75c7\u5019\u6027\u3066\u3093\u304b\u3093\u304c\u521d\u767a\u75c7\u72b6\u3067\u3059<\/li>\n<li>\u8133\u5e79\u90e8\u3068\u5c0f\u8133\u306f\u5897\u5927\u3059\u308b\u3068\u982d\u84cb\u5185\u5727\u4ea2\u9032\u75c7\u72b6\u304c\u3067\u307e\u3059<\/li>\n<li>T2 FLAIR\u3067\u3073\u307e\u3093\u6027\u306e\u9ad8\u4fe1\u53f7\u3068\u306a\u308a\uff0c\u30ac\u30c9\u30ea\u30cb\u30a6\u30e0\u3067\u307e\u3060\u3089\u306b\u5897\u5f37\u3055\u308c\u308b\u3053\u3068\u304c\u3042\u308a\u307e\u3059<\/li>\n<li>\u6cbb\u7642\u306f\uff0c\u5916\u79d1\u6458\u51fa\u3067\u3059\u304c\uff0c\u6458\u51fa\u3067\u304d\u306a\u3044\u90e8\u4f4d\u306e\u3082\u306e\u3082\u591a\u3044\u3067\u3059<\/li>\n<li><i>BRAF<\/i> V600E\u306b\u5909\u7570\u304c\u3042\u308b\u3082\u306e\u306f\u5206\u5b50\u6a19\u7684\u6cbb\u7642\u304c\u53ef\u80fd\u3067\u3059<\/li>\n<\/ul>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<h5><span style=\"color: #003366;\"><strong>\u8133\u5ba4\u5185\u904e\u8aa4\u816b hamartoma of the \u00a0ventricle<\/strong><\/span><\/h5>\n<p>\u8133\u306e\u904e\u8aa4\u816b\u306b\u306f\u8996\u5e8a\u4e0b\u90e8\u306b\u3067\u304d\u308b\u3082\u306e\u3068\u6a4b\u5ef6\u9ac4\u80cc\u5074\u306b\u3067\u304d\u308b\u3082\u306e\u304c\u3042\u308a\u307e\u3059\u3002\u4ee5\u4e0b\u306b\u75c7\u72b6\u306e\u5bfe\u6bd4\u3092\u4e26\u3079\u3066\u304a\u304d\u307e\u3059\u3002\u4e21\u8005\u3068\u3082\u306b\u767a\u4f5c\u304c\u30b3\u30f3\u30c8\u30ed\u30fc\u30eb\u3067\u304d\u306a\u304f\u3066\u6fc0\u3057\u304f\u306a\u308b\u3068\uff0c<strong><span style=\"color: #003366;\">\u75c7\u72b6\u306f\u91cd\u75c7\u5316\u3057\u3066\u884c\u304f<\/span><\/strong>\u306e\u3067\uff0c\u53ef\u80fd\u3067\u3042\u308c\u3070\u5916\u79d1\u6cbb\u7642\u3092\u3057\u305f\u65b9\u304c\u3088\u3044\u3082\u306e\u3067\u3059\u3002\u3067\u3082\u96e3\u3057\u3044\u3002<\/p>\n<h5><b>\u7b2c\uff13\u8133\u5ba4\u5e8a\u904e\u8aa4\u816b (\u8996\u5e8a\u4e0b\u90e8\u904e\u8aa4\u816b\uff09<\/b><b>hypothalamic hamartoma<br \/>\n<\/b><br \/>\n<a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/hamartoma\/\">\u5225\u30da\u30fc\u30b8\u306b\u8a73\u7d30\u304c\u3042\u308b\u306e\u3067\u3053\u3053\u3092\u30af\u30ea\u30c3\u30af<\/a><\/h5>\n<p><b>\u7b11\u3044\u767a\u4f5c\uff0c<\/b><b>\u601d\u6625\u671f\u65e9\u767a\uff0c<\/b><b>\u591a\u52d5\u30fb\u6613\u8208\u596e\u6027\uff0c<\/b><b>\u884c\u52d5\u7570\u5e38\uff0c<\/b><b>\u96e3\u6cbb\u6027\u3066\u3093\u304b\u3093\uff0c<\/b><b>\u610f\u8b58\u6e1b\u640d\uff0c<\/b><b>\u8a8d\u77e5\u6a5f\u80fd\u969c\u5bb3<\/b><\/p>\n<h5><b>\u7b2c\uff14\u8133\u5ba4\u5e8a\u904e\u8aa4\u816b (\u8133\u5e79\u90e8\u904e\u8aa4\u816b\uff09<\/b><b>brainstem hamartoma<\/b><\/h5>\n<p><b>\u9854\u9762\u7b4b\u7570\u5e38\u904b\u52d5\uff0c<\/b><b>\u773c\u7403\u904b\u52d5\u969c\u5bb3\u30fb\u773c\u632f\uff0c<\/b><b>\u81ea\u5f8b\u795e\u7d4c\u969c\u5bb3\uff0c\u767a\u4f5c\u6027\u5614\u5410\uff0c<\/b><b>\u4e0d\u898f\u5247\u547c\u5438\uff0c<\/b><b>\u7247\u9ebb\u75fa\uff0c<\/b><b>\u610f\u8b58\u6e1b\u640d\uff0c<\/b><b>\u9077\u5ef6\u6027\u610f\u8b58\u969c\u5bb3<\/b><\/p>\n<h4>\u7b2c\uff14\u5ba4\u5e8a\u904e\u8aa4\u816b\u306e\u5178\u578b\u4f8b\u3067\u3059<\/h4>\n<p>\u65b0\u751f\u5150\u671f\u3088\u308a\u52d5\u4f5c\u505c\u6b62\u3068\u53f3\u773c\u77bc\u306e\u3061\u304f\u6426\uff0c4\u30f6\u6708\u3067\u53f3\u773c\u306e\u9589\u773c\u3068\u53e3\u89d2\u306e\u5f15\u304d\u3064\u308c\uff08\u9854\u9762\u3051\u3044\u308c\u3093\uff09\u304c\u76ee\u7acb\u3064\u3088\u3046\u306b\u306a\u308a\u307e\u3057\u305f\u30022\u6b73\u6642\u306b\u306f\u6570\u5341\u79d2\u3054\u3068\u306b\u767a\u4f5c\u3092\u7e70\u308a\u8fd4\u3057\u3066\u3044\u307e\u3057\u305f\u3002<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"size-thumbnail wp-image-8367 alignnone\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata1-200x200.jpg\" alt=\"hamarotomata1\" width=\"200\" height=\"200\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata1-200x200.jpg 200w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata1-144x144.jpg 144w\" sizes=\"auto, (max-width: 200px) 100vw, 200px\" \/><img loading=\"lazy\" decoding=\"async\" class=\"size-thumbnail wp-image-8368 alignnone\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata2-200x200.jpg\" alt=\"hamarotomata2\" width=\"200\" height=\"200\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata2-200x200.jpg 200w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata2-144x144.jpg 144w\" sizes=\"auto, (max-width: 200px) 100vw, 200px\" \/><img loading=\"lazy\" decoding=\"async\" class=\"size-thumbnail wp-image-8369 alignnone\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata3-200x200.jpg\" alt=\"hamarotomata3\" width=\"200\" height=\"200\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata3-200x200.jpg 200w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata3-144x144.jpg 144w\" sizes=\"auto, (max-width: 200px) 100vw, 200px\" \/><br \/>\nMRI\u3067\u306f\u6a4b\u306e\u80cc\u5074\uff08\u7b2c4\u8133\u5ba4\u5e8a\uff09\u306bT1\/T2\u3067\u7b49\u4fe1\u53f7\u306e\u9686\u8d77\uff08\u816b\u7624\uff09\u304c\u307f\u3089\u308c\u307e\u3057\u305f\u3002<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-large wp-image-8370\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata6-550x214.jpg\" alt=\"hamarotomata6\" width=\"550\" height=\"214\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata6-550x214.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata6-300x116.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata6-768x298.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata6.jpg 850w\" sizes=\"auto, (max-width: 550px) 100vw, 550px\" \/><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-large wp-image-8371\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata7-550x229.jpg\" alt=\"hamarotomata7\" width=\"550\" height=\"229\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata7-550x229.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata7-300x125.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata7-768x320.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata7.jpg 850w\" sizes=\"auto, (max-width: 550px) 100vw, 550px\" \/><\/p>\n<p>\u624b\u8853\u4e2d\u306e\u9854\u9762\u7b4b\u96fb\u653e\u96fb\u3092\u30e2\u30cb\u30bf\u30fc\u3057\u305f\u3082\u306e\u3067\u3059\u3002\u904e\u8aa4\u816b\u306e\u6458\u51fa\u306b\u3088\u3063\u3066\u6c88\u9759\u5316\u6d88\u5931\u3057\u3066\u3044\u307e\u3059\u3002<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"size-thumbnail wp-image-8372 alignnone\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata4-200x200.jpg\" alt=\"hamarotomata4\" width=\"200\" height=\"200\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata4-200x200.jpg 200w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata4-300x300.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata4-144x144.jpg 144w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata4.jpg 539w\" sizes=\"auto, (max-width: 200px) 100vw, 200px\" \/><img loading=\"lazy\" decoding=\"async\" class=\"size-thumbnail wp-image-8373 alignnone\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata5-200x200.jpg\" alt=\"hamarotomata5\" width=\"200\" height=\"200\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata5-200x200.jpg 200w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamarotomata5-144x144.jpg 144w\" sizes=\"auto, (max-width: 200px) 100vw, 200px\" \/><br \/>\n\u7d50\u679c\u7684\u306b\u904e\u8aa4\u816b\u3092\u307b\u307c\u5168\u6458\u51fa\u3057\u3066\u3057\u307e\u3063\u305f\u306e\u3067\u3059\u304c\uff0c\u8133\u5e79\u80cc\u5074\u306a\u306e\u3067\u795e\u7d4c\u6838\u640d\u50b7\u306e\u30ea\u30b9\u30af\u3092\u4f34\u3044\u307e\u3059\u3002\u4e9c\u5168\u6458\u51fa\u3067\u3082\u767a\u4f5c\u306f\u6b62\u307e\u308b\u3068\u3055\u308c\u3066\u3044\u307e\u3059\u3002\u624b\u8853\u4e2d\u306e\u30e2\u30cb\u30bf\u30fc\u3067\u653e\u96fb\u304c\u7121\u304f\u306a\u308c\u3070\u305d\u3053\u3067\u904e\u8aa4\u816b\u306e\u6458\u51fa\u3092\u4e2d\u6b62\u3057\u3066\u826f\u3044\u306e\u3067\u3057\u3087\u3046\u3002<\/p>\n<h5><span style=\"color: #003366;\">\u76ae\u8cea\u5f62\u6210\u7570\u5e38\uff08\u76ae\u8cea\u7570\u5f62\u6210\uff09\uff0c\u7570\u6240\u6027\u7070\u767d\u8cea\u3068\u306e\u533a\u5225<\/span><\/h5>\n<p><a href=\"\/sawamura\/pediattumor\/corticaldysplasia\/\">\uff08\u8a73\u3057\u304f\u306f\u3053\u3053\u3092\u30af\u30ea\u30c3\u30af\uff09<\/a><\/p>\n<ul>\n<li>\u904e\u8aa4\u816b\u306f\u5148\u5929\u7684\u306a\u904e\u5f62\u6210\uff0c\u76ae\u8cea\u7570\u5f62\u6210\u306f\u5148\u5929\u7684\u306a\u5f62\u6210\u7570\u5e38\u3068\u3055\u308c\u308b\u306e\u3067\u3059\u304c\uff0c\u4e21\u8005\u306e\u533a\u5225\u306f\u5fc5\u305a\u3057\u3082\u5883\u754c\u304c\u3042\u308b\u308f\u3051\u3067\u306f\u3042\u308a\u307e\u305b\u3093<\/li>\n<li>\u300c\u7570\u6240\u6027\u7070\u767d\u8cea\u300d\u3068\u300c\u7070\u767d\u8cea\u3092\u7d44\u7e54\u50cf\u3068\u3059\u308b\u904e\u8aa4\u816b\u300d\u306f\u540c\u3058\u3088\u3046\u306a\u3082\u306e\u3067\u3059<\/li>\n<li>\u6700\u8fd1\uff0c\u3066\u3093\u304b\u3093\u3092\u8a3a\u308b\u3053\u3068\u304c\u597d\u304d\u306a\u304a\u533b\u8005\u3055\u3093\u304c\uff0c\u76ae\u8cea\u7570\u5f62\u6210 cortical dysplasia type IIIb \u306b\uff0cDNT\u3084\u795e\u7d4c\u7bc0\u81a0\u816b\u306a\u3069\u3082\u3072\u3063\u304f\u308b\u3081\u308b\u3053\u3068\u306b\u6c7a\u3081\u307e\u3057\u305f\uff0c\u305d\u308c\u306f\u3061\u3087\u3063\u3068\u4e71\u66b4\u3067\u3059<\/li>\n<li>\u5178\u578b\u7684\u306a\u76ae\u8cea\u7570\u5f62\u6210 classical cortical dysplasia \u4ee5\u5916\u306f\uff0c\u306a\u306b\u3082\u304b\u3082\u76ae\u8cea\u7570\u5f62\u6210\u3068\u547c\u3070\u306a\u3044\u65b9\u304c\u3044\u3044\u3067\u3057\u3087\u3046<\/li>\n<\/ul>\n<h4>\u75c5\u7406\u8a3a\u65ad\u540d\u304c\u78ba\u5b9a\u3067\u304d\u306a\u3044\u69d8\u306a\u5c0f\u5150\u306e\u3066\u3093\u304b\u3093\u539f\u6027\u816b\u760d<\/h4>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyt2.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-18896\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyt2-300x300.jpg\" alt=\"\" width=\"300\" height=\"300\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyt2-300x300.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyt2-550x551.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyt2-200x200.jpg 200w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyt2-768x769.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyt2.jpg 850w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyflair.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-18897\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyflair-292x300.jpg\" alt=\"\" width=\"292\" height=\"300\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyflair-292x300.jpg 292w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyflair-550x566.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyflair-768x790.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyflair.jpg 850w\" sizes=\"auto, (max-width: 292px) 100vw, 292px\" \/><\/a><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyciss.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-18898\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyciss-300x284.jpg\" alt=\"\" width=\"300\" height=\"284\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyciss-300x284.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyciss-550x520.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyciss-768x726.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkyciss.jpg 850w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkygd.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-18900\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkygd-300x294.jpg\" alt=\"\" width=\"300\" height=\"294\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkygd-300x294.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkygd-550x538.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkygd-768x752.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/glioneuronalkygd.jpg 850w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><\/p>\n<p>\u53f3\u5074\u982d\u8449\u5148\u7aef\u306e\u816b\u760d\u3067\u3059\u3002\u767a\u75c7\u6642\u306b\u306fMRI\u3067\u7570\u5e38\u6240\u898b\u304c\u3042\u308a\u307e\u305b\u3093\u3067\u3057\u305f\u304c\uff0c\u5f90\u3005\u306b\u9855\u5728\u5316\u3057\u307e\u3057\u305f\u3002\u30ac\u30c9\u30ea\u30cb\u30a6\u30e0\u5897\u5f37\u306f\u306a\u304f\u4e00\u90e8\u306e\u3046\u80de\u6027\u3067\u3059\u3002<br \/>\n4\u6b73\u6642\u306b\u610f\u8b58\u73fe\u5b58\u3092\u4f34\u3046\u767a\u4f5c\u304c1\u65e53\u56de\u304f\u3089\u3044\u3042\u308b\u3068\u3044\u3046\u96e3\u6cbb\u6027\u90e8\u5206\u3066\u3093\u304b\u3093\u3067\u767a\u75c7\u3057\u307e\u3057\u305f\u3002\u624b\u8853\u4e2d\u306e\u982d\u84cb\u5185\u8133\u6ce2\u3067\uff0c\u4e0b\u5074\u982d\u56de\u306b\u6fc0\u3057\u3044\u68d8\u6ce2\u3068\u68d8\u5f8b\u52d5\u3092\u8a8d\u3081\uff0c\u6241\u6843\u4f53\u3078\u306e\u523a\u5165\u96fb\u6975\u3067\u3082\u68d8\u6ce2\u304c\u3042\u308a\u307e\u3057\u305f\u3002\u5468\u8fba\u8133\u306b\u3082\u68d8\u6ce2\u306f\u3042\u308a\u307e\u3057\u305f\u304c\uff0c\u75c5\u5909\uff08\u816b\u760d\uff09\u3068\u6241\u6843\u4f53\u3092\u5207\u9664\u3059\u308b\u306e\u307f\u306e\u624b\u8853\u3092\u884c\u3044\u307e\u3057\u305f (lesionectomy and amygdalectomy)\u3002\u624b\u8853\u5f8c13\u5e74\u304c\u7d4c\u904e\u3057\u307e\u3059\u304c\u767a\u4f5c\u306f\u3042\u308a\u307e\u305b\u3093\u3002\u75c5\u7406\u3067\u306f\uff0c\u816b\u760d\u7d44\u7e54\u5185\u306b\u795e\u7d4c\u7bc0\u7d30\u80de\u306f\u306a\u304f\uff0c\u76ae\u8cea\u7570\u5f62\u6210 cortical dysplasia\u3042\u308b\u3044\u306f\u30b0\u30ea\u30aa\u30fc\u30de\u69d8\u75c5\u5909 gliomatous lesion\u3068\u3044\u3046\u8a3a\u65ad\u3067\u3057\u305f\u30021p\/19q\u306b\u6b20\u5931\u306f\u3042\u308a\u307e\u305b\u3093\u3067\u3057\u305f\u304c\uff0c\u4e4f\u7a81\u8d77\u81a0\u816b\u3082\u5426\u5b9a\u3067\u304d\u306a\u3044\u5468\u56f2\u7070\u767d\u8cea\u306b\u6d78\u6f64\u6027\u306e\u816b\u760d\u3067\u3057\u305f\u3002\u3053\u306e\u4f8b\u306flow-grade glioma\u3067\u3057\u3087\u3046\u304c\u78ba\u5b9a\u75c5\u7406\u8a3a\u65ad\u306f\u3067\u304d\u306a\u3044\u3082\u306e\u3067\u3059\u3002\u3069\u3061\u3089\u3067\u3042\u3063\u3066\u3082\uff0c\u57fa\u672c\u7684\u306b\u30b0\u30ec\u30fc\u30c91\u3067\u3059\u304b\u3089\uff0c\u624b\u8853\u5f8c\u518d\u767a\u306f\u3057\u307e\u305b\u3093\u3002<\/p>\n<h4>\u4e73\u5150\u671f\u306b\u3066\u3093\u304b\u3093\u767a\u4f5c\u3067\u767a\u75c7\u3059\u308b\u5185\u5074\u5074\u982d\u8449\u904e\u8aa4\u816b<br \/>\nmesial temporal hamartomatous tumor<\/h4>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum12.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft wp-image-16858 size-medium\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum12-300x291.jpg\" alt=\"\" width=\"300\" height=\"291\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum12-300x291.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum12-550x533.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum12-768x745.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum12.jpg 850w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum11.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-16859\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum11-296x300.jpg\" alt=\"\" width=\"296\" height=\"300\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum11-296x300.jpg 296w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum11-550x557.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum11-768x778.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum11.jpg 850w\" sizes=\"auto, (max-width: 296px) 100vw, 296px\" \/><\/a><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum2.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-16860\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum2-298x300.jpg\" alt=\"\" width=\"298\" height=\"300\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum2-298x300.jpg 298w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum2-550x553.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum2-200x200.jpg 200w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum2-768x773.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum2.jpg 850w\" sizes=\"auto, (max-width: 298px) 100vw, 298px\" \/><\/a><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum3.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-16861\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum3-300x300.jpg\" alt=\"\" width=\"300\" height=\"300\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum3-300x300.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum3-200x200.jpg 200w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum3.jpg 850w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><\/p>\n<p>\u4e73\u5150\u671f\u306b\u5168\u8eab\u6027\u611f\u5e2f\u75d9\u6523\u767a\u4f5c\u3067\u767a\u75c7\u3057\u307e\u3057\u305f\u3002\u5de6\u6d77\u99ac\u920e\u306b\u5f37\u3044\u77f3\u7070\u5316\u304c\u3042\u308a\u307e\u3059\u3002\u5074\u982d\u8449\u786c\u5316\u75c7\u3068\u3082\u8a00\u308f\u308c\u308b\u3082\u306e\u3067\u3059\u3002\u3053\u306e\u90e8\u4f4d\u306e\u904e\u8aa4\u816b\u69d8\u306e\u816b\u760d\u306f\u96e3\u6cbb\u6027\u3066\u3093\u304b\u3093\u3068\u306a\u308b\u3053\u3068\u304c\u591a\u304f\uff0c\u75c5\u5909\u5207\u9664\u304c\u5fc5\u8981\u3068\u306a\u308a\u307e\u3059\u3002<\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-large wp-image-16863\" src=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum4-1-550x237.jpg\" alt=\"\" width=\"550\" height=\"237\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum4-1-550x237.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum4-1-300x130.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum4-1-768x332.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/hamartomaum4-1.jpg 850w\" sizes=\"auto, (max-width: 550px) 100vw, 550px\" \/><\/p>\n<p>\u8133\u6ce2\u3067\u306f\u524d\u982d\u8449\u306b\u8540\u5f8b\u52d5\u3092\u8a8d\u3081\u307e\u3059\u3002\u5207\u9664\u306f\u6241\u6843\u4f53\u3068\u6d77\u99ac\u920e\u306e\u6458\u51fa\u3092\u76ee\u6307\u3059\u3082\u306e\u3067\u3059\u3002<\/p>\n<hr \/>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-medium wp-image-8377\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/sparrows-300x196.jpg\" alt=\"sparrows\" width=\"300\" height=\"196\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/sparrows-300x196.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/sparrows-768x501.jpg 768w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/sparrows-550x359.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2014\/10\/sparrows.jpg 827w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/p>\n","protected":false},"excerpt":{"rendered":"<p>glioneuronal and neuronal tumors \u3066\u3093\u304b\u3093\u306e\u539f\u56e0\u3068\u306a\u308b WHO \u30b0\u30ec\u30fc\u30c91 \u306e\u826f\u6027\u816b\u760d\u306e\u7fa4\u3067\u3059 \u75c5\u7406\u78ba\u5b9a\u8a3a\u65ad\u304c\u3064\u304b\u305a\uff0c\u904e\u8aa4\u816b hamartoma \u76ae\u8cea\u5f62\u6210\u7570\u5e38 cortical dyspl [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[5],"tags":[],"class_list":["post-6289","post","type-post","status-publish","format-standard","hentry","category-pediattumor"],"aioseo_notices":[],"_links":{"self":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/6289","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/comments?post=6289"}],"version-history":[{"count":49,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/6289\/revisions"}],"predecessor-version":[{"id":23658,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/6289\/revisions\/23658"}],"wp:attachment":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/media?parent=6289"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/categories?post=6289"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/tags?post=6289"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}