{"id":1867,"date":"2013-01-14T09:36:54","date_gmt":"2013-01-14T00:36:54","guid":{"rendered":"\/sawamura\/?p=1867"},"modified":"2022-09-27T09:47:29","modified_gmt":"2022-09-27T00:47:29","slug":"2021who","status":"publish","type":"post","link":"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/2021who\/","title":{"rendered":"2021\u5e74 WHO \u8133\u816b\u760d\u75c5\u7406\u5206\u985e"},"content":{"rendered":"<h5>2021\u5e746\u6708\u306b5\u5e74\u3076\u308a\u306b\u6539\u5b9a\u3055\u308c\u307e\u3057\u305f<\/h5>\n<h5><strong>\u591a\u304f\u306e\u816b\u760d\u578b\u3067\u907a\u4f1d\u5b50\u8a3a\u65ad\u304c\u5fc5\u8981\u3068\u306a\u308a\uff0c\u75c5\u7406\u8a3a\u65ad\u540d\u304c\u5909\u308f\u3063\u3066\u3044\u307e\u3059\u304c\uff0c<span style=\"color: #ff0000;\">\u6cbb\u7642\u65b9\u6cd5\u306e\u9032\u6b69\u306f\u8ffd\u3044\u3064\u3044\u3066\u3044\u307e\u305b\u3093<\/span>\uff0c\u3067\u3059\u304b\u3089\u5f53\u9762<span style=\"color: #ff0000;\">\u6cbb\u7642\u306e\u9078\u629e\u306f2016\u5e74\u306e\u65e7\u5206\u985e\u306b\u5f93\u3063\u305f\u65b9\u304c\u3044\u3044<\/span>\u3067\u3057\u3087\u3046<\/strong><\/h5>\n<h5><strong>\u661f\u7d30\u80de\u816bIDH mutant\u306f\uff0c\u30b0\u30ec\u30fc\u30c9\u304c2, 3, 4\u3068\u306a\u308a\uff0c\u3082\u306f\u3084\u4f4e\u60aa\u6027\u5ea6\u30b0\u30ea\u30aa\u30fc\u30de low grade\u3068\u547c\u3079\u306a\u304f\u306a\u3063\u3066\u3057\u307e\u3044\u307e\u3057\u305f<\/strong><\/h5>\n<h5>\u7d44\u7e54\u5f62\u614b\u3068\u907a\u4f1d\u5b50\u30bf\u30a4\u30d7\u304c\u77db\u76fe\u3057\u305f\u3089\u3069\u3046\u3059\u308b\u304b\uff1f<\/h5>\n<ul>\n<li>\u7d44\u7e54\u8a3a\u65ad\u3067\u661f\u7d30\u80de\u816b\u3068\u8a3a\u65ad\u3055\u308c\uff0c\u907a\u4f1d\u5b50\u8a3a\u65ad\u3067 IDH\u5909\u7570\u30681p\/19q\u6b20\u5931\u304c\u3042\u3063\u305f\u3089<\/li>\n<li>\u3053\u306e\u8a3a\u65ad\u306f\uff0c\u4e4f\u7a81\u8d77\u81a0\u816b (IDH\u5909\u7570\u30681p\/19q\u6b20\u5931) \u3068\u306a\u308a\u307e\u3059<\/li>\n<li><strong><span style=\"color: #ff0000;\">the genotype trumps the histological diagnosis<\/span><\/strong>\u3067\u3059<\/li>\n<li>\u30c8\u30e9\u30f3\u30d7(*_*)? \u00a0trump\u3068\u3044\u3046\u306e\u306f\u5965\u306e\u624b\u3092\u51fa\u3057\u3066\u52dd\u3064\u3068\u3044\u3046\u610f\u5473\u3067\u3059<\/li>\n<li>\u30b0\u30ec\u30fc\u30c9\u306f\u7279\u5225\u306a\u3082\u306e\u3092\u9664\u3044\u3066\u4ee5\u524d\u3068\u540c\u3058\u7d44\u7e54\u8a3a\u65ad\u3067\uff0c\u30a2\u30e9\u30d3\u30a2\u6570\u5b57 Arabic numecals 1, 2, 3, 4 \u3067\u8a18\u8f09\u3059\u308b\u3053\u3068\u306b\u306a\u308a\u307e\u3057\u305f<\/li>\n<li><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/whograde\/\"><strong>\u60aa\u6027\u5ea6\u3092\u793a\u3059\u30b0\u30ec<span style=\"color: #000080;\">\u30fc\u30c9\u306f\u5225\u30da\u30fc\u30b8\u306b\u307e\u3068\u3081\u3066\u8a18\u8f09\u3057\u3066\u3044\u307e\u3059\uff08\u3053\u3053\u3092\u30af\u30ea\u30c3\u30af\uff09<\/span><\/strong><\/a><\/li>\n<\/ul>\n<h4>2021\u5e74\u5206\u985e\u306e\u8981\u7d04\u304c\u66f8\u304b\u304b\u308c\u3066\u3044\u308b\u53c2\u8003\u6587\u732e<\/h4>\n<p class=\"wi-article-title article-title-main\">Luis DN: The 2021 WHO Classification of Tumors of the Central Nervous System: a summary. Neuro Oncol 2021<\/p>\n<h4><span style=\"color: #000080;\"><strong>NOS not otherwise specific \u3068 NEC not elsewhere classified<\/strong><\/span><\/h4>\n<p>\u907a\u4f1d\u5b50\u8a3a\u65ad\u304c\u5c0e\u5165\u3055\u308c\u305f\u3053\u3068\u306b\u3088\u3063\u3066\uff0c\u907a\u4f1d\u5b50\u8a3a\u65ad\u304c\u884c\u308f\u308c\u305a\u3042\u308b\u3044\u306f\u907a\u4f1d\u5b50\u8a3a\u65ad\u304c\u5408\u81f4\u3057\u306a\u304f\u3066\u8a3a\u65ad\u3067\u304d\u306a\u3044\u4f8b\u304c\u767a\u751f\u3057\u307e\u3057\u305f\u3002\u3053\u308c\u3092<span style=\"color: #ff0000;\"><strong>NOS<\/strong><\/span>\u3068\u3044\u3044\u307e\u3059\u3002\u4e00\u65b9\uff0cWHO\u306e\u3069\u306e\u5206\u985e\u306b\u3082\u5165\u3089\u306a\u3044\u3082\u306e\u3092<span style=\"color: #ff0000;\"><strong>NEC<\/strong><\/span>\u3068\u3044\u3044\u307e\u3059\u3002\u305f\u3068\u3048\u3070\uff0c\u7d44\u7e54\u8a3a\u65ad\u3067\u3073\u307e\u3093\u6027\u661f\u7d30\u80de\u816b\u30b0\u30ec\u30fc\u30c92\u3067IDH\u91ce\u751f\u578b\uff0c\u3067\u3082\u4ed6\u306e\u907a\u4f1d\u5b50\u5909\u7570\u304c\u306a\u304f\u3066\u81a0\u82bd\u816b\u306b\u3082\u5206\u985e\u3067\u304d\u306a\u3044\u3082\u306e\u306f\uff0c\u661f\u7d30\u80de\u816bIDH\u91ce\u751f\u578b\u30b0\u30ec\u30fc\u30c92 NOS\u3067\u3059\u3002NEC\u306e\u4e2d\u306b\u306f\uff0c\u75c5\u7406\u8a3a\u65ad\u304c\u9069\u5207\u306b\u306a\u3055\u308c\u3066\u3082\uff0c\u81e8\u5e8a\u50cf\u3068\u5168\u304f\u5408\u81f4\u3057\u306a\u3044\u3068\u3044\u3046\u3082\u306e\u3082\u542b\u307e\u308c\u307e\u3059\u3002\u305f\u3068\u3048<span style=\"color: #000080;\"><strong>\u5206\u5b50<\/strong><strong>\u75c5\u7406\u78ba\u5b9a\u8a3a\u65ad\u304c\u3067\u3066\u3082\uff0c\u60a3\u8005\u3055\u3093\u306e\u81e8\u5e8a\u50cf\u3068\u5168\u304f\u4e00\u81f4\u3057\u306a\u3044\u6642\u306b\u306fNEC\u3068\u3064\u3051\u3066\u75c5\u7406\u8a3a\u65ad\u306f\uff0cdescriptive diagnosis\u3068\u3057\u3066\u7559\u3081\u305f\u65b9\u304c\u3044\u3044<\/strong><\/span>\u3067\u3059\u3002<\/p>\n<div>\n<hr \/>\n<h3><span style=\"color: #000080;\">\u30b0\u30ea\u30aa\u30fc\u30de\uff0c\u30b0\u30ea\u30a2\u795e\u7d4c\u7d30\u80de\u816b\u760d\uff0c\u795e\u7d4c\u7d30\u80de\u816b<br \/>\n<\/span><span style=\"color: #000080;\">Glioma, glioneuronal tumors,and neuronal tumors<\/span><\/h3>\n<h5>\u6210\u4eba\u3073\u307e\u3093\u6027\u30b0\u30ea\u30aa\u30fc\u30de\u30002021\u5e74\u306e\u5206\u985e\u306f3\u7a2e\u985e<br \/>\nAdult-type diffuse gliomas<\/h5>\n<\/div>\n<p><span style=\"color: #000080;\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/diffuseastrocytoma\/\">\u661f\u7d30\u80de\u816b IDH\u5909\u7570\u578b<\/a><\/span>\u00a0(\u30b0\u30ec\u30fc\u30c92, 3, 4)<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Astrocytoma, IDH mutant<\/strong><\/span>, nuclear ATRX lost<\/p>\n<p><span style=\"color: #000080;\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/olig\/\">\u4e4f\u7a81\u8d77\u81a0\u816b IDH\u5909\u7570\u578b\uff0c1p\/19q\u5171\u6b20\u5931<\/a>\u00a0<\/span>(\u30b0\u30ec\u30fc\u30c92, 3)<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Oligodendroglioma, IDH mutant, 1p\/19q-codeleted<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/glioblastom\/\"><span style=\"color: #000080;\">\u81a0\u82bd\u816b IDH\u91ce\u751f\u578b<\/span><\/a>\u00a0(\u30b0\u30ec\u30fc\u30c94)<\/strong><\/span><br \/>\n<strong><span style=\"color: #000080;\">Glioblastoma, IDH wildtype<\/span><\/strong>, nuclear ATRX retained, typical histology or TERT, EGFR, +7\/-10<\/p>\n<p><strong><span style=\"color: #ff0000;\">\u3082\u3063\u3068\u3082\u5927\u304d\u306a\u5909\u66f4\u70b9\u306f\uff0c\u3073\u307e\u3093\u6027\u661f\u7d30\u80de\u816b \u304c \u661f\u7d30\u80de\u816bIDH\u5909\u7570\u578b\u3068\u306a\u308a\uff0c\u9000\u5f62\u6210\u6027\u661f\u7d30\u80de\u816b \u3068 \u9000\u5f62\u6210\u6027\u4e4f\u7a81\u8d77\u81a0\u816b \u306e\u75c5\u540d\u304c\u6d88\u3048\u305f\u3053\u3068\u3067\u3059\u3002<\/span><\/strong><\/p>\n<h5>\u5c0f\u5150\u30bf\u30a4\u30d7\u306e\u3073\u307e\u3093\u6027\u4f4e\u60aa\u6027\u5ea6\u30b0\u30ea\u30aa\u30fc\u30de\u30002021\u5e74\u306e\u5206\u985e\u306f4\u7a2e\u985e<br \/>\nPediatric-type diffuse low-grade gliomas<\/h5>\n<p><span style=\"color: #000080;\"><strong>\u3073\u307e\u3093\u6027\u661f\u7d30\u80de\u816b,\u00a0<em>MYB<\/em>\u3042\u308b\u3044\u306f<em>MYBL1\u00a0<\/em>\u907a\u4f1d\u5b50\u7570\u5e38\u00a0\u00a0(\u30b0\u30ec\u30fc\u30c91)<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Diffuse astrocytoma, <em>MYB<\/em> or <em>MYBL1<\/em>-altered<\/strong><\/span><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/hamartomas\/\"><span style=\"color: #000080;\"><strong>\u8840\u7ba1\u4e2d\u5fc3\u6027\u81a0\u816b \u30a2\u30f3\u30b8\u30aa\u30bb\u30f3\u30c8\u30ea\u30c3\u30af\u30fb\u30b0\u30ea\u30aa\u30fc\u30de<\/strong><\/span><\/a><span style=\"color: #000080;\"><strong>\u00a0 (\u30b0\u30ec\u30fc\u30c91)<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Angiocentric glioma<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/hamartomas\/\">Polymorphous low-grade neuroepithelial tumor of the young<\/a>\u00a0 (\u30b0\u30ec\u30fc\u30c91)<\/strong><\/span><\/p>\n<p><strong><span style=\"color: #000080;\">MAPK pathway\u7570\u5e38\u304c\u3042\u308b\u3073\u307e\u3093\u6027\u4f4e\u60aa\u6027\u5ea6\u30b0\u30ea\u30aa\u30fc\u30de<br \/>\nDiffuse low-grade glioma, MAPK pathway-altered<\/span><\/strong><\/p>\n<h5><a title=\"\u5c0f\u5150\u30bf\u30a4\u30d7\u306e\u3073\u307e\u3093\u6027\u9ad8\u60aa\u6027\u5ea6\u30b0\u30ea\u30aa\u30fc\u30de Pediatric-type diffuse high-grade gliomas\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/pediatricdiffusehighgrageglioma\/\">\u5c0f\u5150\u30bf\u30a4\u30d7\u306e\u3073\u307e\u3093\u6027\u9ad8\u60aa\u6027\u5ea6\u30b0\u30ea\u30aa\u30fc\u30de<\/a>\u30002021\u5e74\u306e\u5206\u985e\u306f4\u7a2e<br \/>\nPediatric-type diffuse high-grade gliomas<\/h5>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/diffusemidlineglioma\/\"><strong><span style=\"color: #000080;\">\u3073\u307e\u3093\u6027\u6b63\u4e2d\u30b0\u30ea\u30aa\u30fc\u30de\u00a0 H3 K27\u907a\u4f1d\u5b50\u7570\u5e38<\/span><\/strong><\/a>\u00a0(\u30b0\u30ec\u30fc\u30c94)<br \/>\n<span style=\"color: #000080;\"><strong>Diffuse midline glioma<\/strong><\/span>, <span style=\"color: #000080;\"><strong>H3 K27-altered,\u00a0<\/strong><\/span>IDH wildtype, nuclear ATRX retained<\/p>\n<p><span style=\"color: #000080;\"><strong>\u3073\u307e\u3093\u6027\u534a\u7403\u6027\u30b0\u30ea\u30aa\u30fc\u30de\u00a0H3.3 G34\u5909\u7570\u578b<\/strong><\/span>\u00a0(\u30b0\u30ec\u30fc\u30c94)<br \/>\n<strong><span style=\"color: #000080;\">Diffuse hemispheric\u00a0<\/span><\/strong><span style=\"color: #000080;\"><span style=\"caret-color: #000080;\"><b>glioma<\/b><\/span><\/span>, <span style=\"color: #000080;\"><strong>H3.3 G34 mutant,\u00a0<\/strong><\/span>IDH wildtype, nuclear ATRX lost, age&lt;50<\/p>\n<p><span style=\"color: #000080;\"><strong>\u3073\u307e\u3093\u6027\u5c0f\u5150\u9ad8\u60aa\u6027\u5ea6\u30b0\u30ea\u30aa\u30fc\u30de\u00a0(\u30b0\u30ec\u30fc\u30c94)<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Diffuse pediatric-type high-grade glioma, \u00a0H3-wildtype and IDH-wildtype<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>\u4e73\u5150\u534a\u7403\u6027\u30b0\u30ea\u30aa\u30fc\u30de<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Infant-type hemispheric glioma<\/strong><\/span><\/p>\n<h5>\u5883\u754c\u660e\u77ad\u306a\u661f\u7d30\u80de\u7cfb\u30b0\u30ea\u30aa\u30fc\u30de\uff08\u3073\u307e\u3093\u6027\u3067\u306f\u306a\u3044\uff09<br \/>\nCircumscribed astrocytic gliomas<\/h5>\n<p><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" title=\"\u6bdb\u69d8\u7d30\u80de\u6027\u661f\u7d30\u80de\u816b\" href=\"\/sawamura\/pediattumor\/pilo\/\">\u6bdb\u69d8\u7d30\u80de\u6027\u661f\u7d30\u80de\u816b<\/a><br \/>\nPilocytic astrocytoma (\u30b0\u30ec\u30fc\u30c91)\u3000<\/span><\/strong><\/p>\n<p><strong><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/pilo\/\"><span style=\"color: #000080;\"><span style=\"caret-color: #000080;\">piloid-features\u3092\u542b\u3080\u9ad8\u60aa\u6027\u5ea6\u661f\u7d30\u80de\u816b (\u30b0\u30ec\u30fc\u30c94)<\/span><\/span><\/a><br \/>\n<span style=\"color: #000080;\">High-grade astrocytoma with piloid features<\/span><\/strong><\/p>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/glioma\/pleomorphicxantho\/\">\u591a\u578b\u9ec4\u8272\u661f\u7d30\u80de\u816b<\/a><\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Pleomorphic xanthoastrocytoma (\u30b0\u30ec\u30fc\u30c9 2, 3)<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/pediattumor\/subepgiantastro\/\">\u4e0a\u8863\u4e0b\u5de8\u7d30\u80de\u6027\u661f\u7d30\u80de\u816b (\u30b0\u30ec\u30fc\u30c91)<\/a><\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Subependymal \u00a0giant cell astrocytoma SEGA<\/strong><\/span><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/chordoidglioma\/\"><span style=\"color: #000080;\"><strong>\u810a\u7d22\u816b\u69d8\u81a0\u816b \u30b3\u30eb\u30c9\u30a4\u30c9\u30fb\u30b0\u30ea\u30aa\u30fc\u30de (\u30b0\u30ec\u30fc\u30c91)<\/strong><\/span><\/a><br \/>\n<span style=\"color: #000080;\"><strong>Chordoid glioma<\/strong><\/span><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/astroblastoma\/\"><span style=\"color: #000080;\"><strong>\u661f\u82bd\u816b, <em>MN1<\/em>-\u907a\u4f1d\u5b50\u7570\u5e38<\/strong><\/span><\/a><br \/>\n<span style=\"color: #000080;\"><strong>Astroblastoma, <em>MN1<\/em>-altered<\/strong><\/span><\/p>\n<hr \/>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong>\u30b0\u30ea\u30a2\u795e\u7d4c<\/strong><\/span><span style=\"color: #000080;\"><strong>\u7d30\u80de\u3068\u795e\u7d4c\u7d30\u80de\u3092\u8d77\u6e90\u3068\u3059\u308b\u816b\u760d<br \/>\n<\/strong><\/span><span style=\"color: #000080;\"><strong>\u00a0 Glioneuronal and neuronal tumors<\/strong><br \/>\n<\/span><\/h3>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/gangliocyto\/\"><span style=\"color: #000080;\"><strong>\u795e\u7d4c\u7bc0\u81a0\u816b\u00a0(\u30b0\u30ec\u30fc\u30c91, 3)<\/strong><\/span><\/a><br \/>\n<span style=\"color: #000080;\"><strong>Ganglioglioma<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"\/sawamura\/pediattumor\/desmoinfantile\/\">\u7dda\u7dad\u5f62\u6210\u6027<\/a><a style=\"color: #000080;\" href=\"\/sawamura\/pediattumor\/desmoinfantile\/\">\u4e73\u5150<\/a><a style=\"color: #000080;\" href=\"\/sawamura\/pediattumor\/desmoinfantile\/\">\u795e\u7d4c\u7bc0\u81a0\u816b<\/a><\/span><a style=\"color: #000080;\" href=\"\/sawamura\/pediattumor\/desmoinfantile\/\"><span style=\"color: #000080;\">\uff0f\u661f\u7d30\u80de\u816b<\/span><\/a>\u00a0<\/strong><\/span><span style=\"color: #000080;\"><strong>(\u30b0\u30ec\u30fc\u30c91)<\/strong><strong><br \/>\n<span style=\"color: #000080;\">Desmoplastic infantile ganglioglioma \/ desmoplastic infantile astrocytoma \u00a0<\/span>DIA\/DIG<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/glioma\/neurocyto\/\">\u80da<\/a><\/span><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/glioma\/neurocyto\/\"><span style=\"color: #000080;\">\u82bd\u7570\u5f62\u6210\u6027\u795e\u7d4c\u4e0a\u76ae\u816b\u760d DNT<\/span><\/a> (\u30b0\u30ec\u30fc\u30c91)<a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/glioma\/neurocyto\/\"><br \/>\n<\/a>Dysembryoplastic neuroepithelial tumor\u3000DNT<\/strong><\/span><\/p>\n<p align=\"left\"><em><span style=\"color: #000080;\"><strong>Diffuse glioneuronal tumor with oligodendroglioma-like features and nuclear clusters<\/strong><\/span><\/em><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>\u4e73\u982d\u72b6\u30b0\u30ea\u30a2\u795e\u7d4c\u7d30\u80de\u816b\u760d (\u30b0\u30ec\u30fc\u30c91)<br \/>\nPapillary glioneuronal tumor<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/rosetteformingtumor\/\">\u30ed\u30bc\u30c3\u30c8\u5f62\u6210\u6027\u30b0\u30ea\u30a2\u795e\u7d4c\u7d30\u80de\u816b\u760d<\/a> \u00a0(\u30b0\u30ec\u30fc\u30c91)<\/span><br \/>\nRosette-forming glioneuronal tumor of the fourth ventricle \u00a0RGNT<br \/>\n<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/myxoid-glioneuronal-tumor\/\"><span style=\"color: #000080;\">\u7c98\u6db2\u72b6\u30b0\u30ea\u30a2\u795e\u7d4c\u7d30\u80de\u816b\u760d<\/span><\/a> \u00a0(\u30b0\u30ec\u30fc\u30c91)<br \/>\nMyxoid glioneuronal tumor<\/strong><\/span><\/p>\n<p align=\"left\"><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/diffuseleptomeningealglioneuronaltumor\/\"><strong><span style=\"color: #000080;\">Diffuse leptomeningeal glioneuronal tumor DLGNT<\/span><\/strong><\/a><\/p>\n<p align=\"left\"><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/gangliocyto\/\"><span style=\"color: #000080;\"><strong>\u795e\u7d4c\u7bc0\u7d30\u80de\u816b <\/strong><\/span><\/a><span style=\"color: #000080;\"><strong>(\u30b0\u30ec\u30fc\u30c91)<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Gangliocytoma<\/strong><\/span><\/p>\n<p><strong><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/hamartomas\/\"><span style=\"color: #000080;\">\u591a\u7d50\u7bc0\u7a7a\u80de\u72b6\u795e\u7d4c\u7d30\u80de\u816b\u760d<\/span><\/a><span style=\"color: #000080;\"> (\u30b0\u30ec\u30fc\u30c9 1)<\/span><br \/>\n<\/strong><strong><span style=\"color: #000080;\"><span style=\"color: #000080;\">Multinodular and vacuolating neuronal tumor \u00a0MVNT<\/span><\/span><\/strong><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" title=\"\u30ec\u30eb\u30df\u30c3\u30c8\u30fb\u30c0\u30af\u30ed\u30b9\u75c5 Lhermitte-Duclos disease\" href=\"\/sawamura\/pediattumor\/lhermitteduclosdisease\/\">\u30ec\u30eb\u30df\u30c3\u30c8\u30fb\u30c0\u30af\u30ed\u30b9\u75c5<\/a><\/span><br \/>\nDysplastic cerebellar gangliocytoma of cerebellum (Lhermitte-Duclos diseaes)<br \/>\n<\/strong><\/span><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/centralneuro\/\">\u4e2d\u67a2\u6027\u795e\u7d4c\u7d30\u80de\u7a2e\uff0c\u30bb\u30f3\u30c8\u30e9\u30eb\u30cb\u30e5\u30fc\u30ed\u30b5\u30a4\u30c8\u30fc\u30de<\/a><br \/>\nCentral neurocytoma (\u30b0\u30ec\u30fc\u30c9 2)<\/span><\/strong><strong><span style=\"color: #000080;\"><br \/>\n<\/span><\/strong><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\">\u8133\u5ba4\u5916\u795e\u7d4c\u7d30\u80de\u816b<br \/>\nExtraventricular neurocytoma (\u30b0\u30ec\u30fc\u30c9 2)\u3000<\/span><\/strong><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>\u5c0f\u8133\u795e\u7d4c\u8102\u80aa\u816b<br \/>\nCerebellar liponeurocytoma (\u30b0\u30ec\u30fc\u30c9 2)<\/strong><\/span><\/p>\n<h3 align=\"left\"><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/ependy\/\"><span style=\"color: #000080;\"><strong>\u4e0a\u8863\u7cfb\u816b\u760d \u00a0<\/strong><\/span><\/a><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/ependy\/\"><span style=\"color: #000080;\"><strong>Ependymal tumors\u3000<\/strong><\/span><\/a><\/h3>\n<p align=\"left\"><strong><span style=\"color: #333399;\">\u30c6\u30f3\u30c8\u4e0a \u4e0a\u8863\u816b<br \/>\nSupratentoirial ependymoma<span style=\"color: #000080;\"> (\u30b0\u30ec\u30fc\u30c9 2, 3)<\/span><\/span><\/strong><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><span style=\"color: #333399;\">\u30c6\u30f3\u30c8\u4e0a \u4e0a\u8863\u816b <em>ZFTA<\/em> fusion-positive<br \/>\nSupratentoirial ependymoma, <em>ZFTA<\/em> fusion-positive<\/span><\/span><\/strong><\/p>\n<p align=\"left\"><strong><span style=\"color: #333399;\">\u30c6\u30f3\u30c8\u4e0a \u4e0a\u8863\u816b <em>YAP1<\/em> fusion-positive<br \/>\nSupratentoirial ependymoma, <em>YAP1<\/em> fusion-positive<\/span><\/strong><\/p>\n<p align=\"left\"><span style=\"color: #333399;\"><span style=\"caret-color: #333399;\"><b>\u5f8c\u982d\u7aa9 \u4e0a\u8863\u816b<br \/>\nPosterior fossa ependymoma<strong><span style=\"color: #000080;\"> (\u30b0\u30ec\u30fc\u30c9 2, 3)<\/span><\/strong><\/b><\/span><\/span><\/p>\n<p align=\"left\"><span style=\"color: #333399;\"><span style=\"caret-color: #333399;\"><b>\u5f8c\u982d\u7aa9 \u4e0a\u8863\u816b PFA\u30b0\u30eb\u30fc\u30d7<br \/>\nPosterior fossa ependymoma, group PFA<\/b><\/span><\/span><\/p>\n<p align=\"left\"><span style=\"color: #333399;\"><span style=\"caret-color: #333399;\"><b>\u5f8c\u982d\u7aa9 \u4e0a\u8863\u816b PFB\u30b0\u30eb\u30fc\u30d7<br \/>\nPosterior fossa ependymoma, group PFB<\/b><\/span><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>\u810a\u9ac4\u4e0a\u8863\u816b<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Spinal ependymoma (\u30b0\u30ec\u30fc\u30c9 2)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>\u810a\u9ac4\u4e0a\u8863\u816b<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Spinal ependymoma, <em>MYCN<\/em>-amplified<\/strong><\/span><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" title=\"\u7c98\u6db2\u4e73\u982d\u72b6\u4e0a\u8863\u816b\" href=\"\/sawamura\/braintumors\/glioma\/myxopapillary\/\">\u7c98\u6db2\u4e73\u982d\u72b6\u4e0a\u8863\u816b<\/a><br \/>\nMyxopapillary ependymoma (\u30b0\u30ec\u30fc\u30c9 2)<br \/>\n<\/span><\/strong><\/p>\n<p align=\"left\"><strong><span style=\"color: #333399;\"><a style=\"color: #333399;\" title=\"\u4e0a\u8863\u4e0b\u816b\" href=\"\/sawamura\/braintumors\/glioma\/subependymoma\/\">\u4e0a\u8863\u4e0b\u816b<\/a><br \/>\nSubependymoma<span style=\"color: #000080;\"> (\u30b0\u30ec\u30fc\u30c9 1)<\/span><br \/>\n<\/span><\/strong><\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong>\u8108\u7d61\u53e2\u816b\u760d\u3000Choroid plexus tumors<\/strong><\/span><\/h3>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" title=\"\u8108\u7d61\u53e2\u4e73\u982d\u816b\" href=\"\/sawamura\/pediattumor\/choroidplexus\/\">\u8108\u7d61\u53e2\u4e73\u982d\u816b<\/a><br \/>\nChoroid plexus papilloma (\u30b0\u30ec\u30fc\u30c9 1)<\/span><\/strong><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" title=\"\u8108\u7d61\u53e2\u4e73\u982d\u816b\" href=\"\/sawamura\/pediattumor\/choroidplexus\/\">\u975e\u5b9a\u578b\u8108\u7d61\u53e2\u4e73\u982d\u816b<\/a><br \/>\nAtypical choroid plexus papilloma (\u30b0\u30ec\u30fc\u30c9 2)<\/span><\/strong><strong><span style=\"color: #000080;\"><br \/>\n<\/span><\/strong><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" title=\"\u8108\u7d61\u53e2\u4e73\u982d\u816b\" href=\"\/sawamura\/pediattumor\/choroidplexus\/\">\u8108\u7d61\u53e2\u764c<br \/>\n<\/a>Choroid plexus carcinoma (grade III)<\/span><\/strong><\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong>\u80ce\u5150\u6027\u816b\u760d\u3000Embryonal tumors<\/strong><\/span><\/h3>\n<h5 align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/pediattumor\/medullo\/\">\u9ac4\u82bd\u816b<\/a><a style=\"color: #000080;\" href=\"\/sawamura\/pediattumor\/medullo\/\">\u00a0\u00a0Medulloblastoma (grade 4)<\/a><\/strong><\/span><\/h5>\n<p align=\"left\"><strong><span style=\"color: #000080;\">Medulloblastomas, molecularly defined \u00a0 \u907a\u4f1d\u5b50\u8a3a\u65ad\u304c\u306a\u3055\u308c\u305f\u3082\u306e<br \/>\n<\/span><\/strong><span style=\"color: #000080;\"><strong>\u00a0 \u00a0Medulloblastoma, WNT activated<br \/>\n<\/strong><\/span>\u00a0 \u00a0 \u00a0 \u00a0WNT activated\u306f\u6cbb\u308a\u3084\u3059\u3044\u306e\u3067\u3059\u304c\uff0c\u30b0\u30ec\u30fc\u30c94\u3067\u3059<br \/>\n<strong><span style=\"color: #000080;\">\u00a0 \u00a0Medulloblastoma, SHH activated and\u00a0<em>TP53<\/em>\u00a0wildtype<br \/>\n<\/span><\/strong><strong><span style=\"color: #000080;\">\u00a0 \u00a0Medulloblastoma, SHH activated and\u00a0<em>TP53<\/em> mutant<br \/>\n<\/span><\/strong><em>\u00a0 \u00a0<\/em><span style=\"color: #000080;\"><strong>Medulloblastoma,\u00a0non-WNT\/non-SHH<\/strong><\/span><em><br \/>\n<\/em><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\">Medulloblastoma histologicaly defined (grade 4)\u3000\u7d44\u7e54\u8a3a\u65ad\u306e\u307f\u306b\u3088\u308b\u3082\u306e<\/span><\/strong><\/p>\n<h5 align=\"left\">\u9ac4\u82bd\u816b\u4ee5\u5916\u306e\u80ce\u5150\u6027\u816b\u760d other CNS embryonal tumors<\/h5>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/atrt\/\">\u975e\u5b9a\u578b\u5947\u5f62\u816b\u69d8\uff0f\u30e9\u30d6\u30c9\u30a4\u30c9\u816b\u760d \u00a0<\/a><\/strong><strong><a style=\"color: #000080;\" title=\"AT\/RT\" href=\"\/sawamura\/pediattumor\/atrt\/\">AT\/RT<\/a><br \/>\nAtypical teratoid\/rhabdoid tumor\u3000AT\/RT (\u30b0\u30ec\u30fc\u30c9 4)<\/strong><\/span><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/atrt\/\"><span style=\"color: #000080;\"><strong><em>Cribriform neuroepithelial tumor<\/em><\/strong><\/span><\/a><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/etmr-etantr\/\"><span style=\"color: #000080;\"><strong>\u591a\u5c64\u6027\u30ed\u30bc\u30c3\u30c8\u3092\u6709\u3059\u308b\u80ce\u5150\u6027\u816b\u760d<br \/>\n<\/strong><\/span><\/a><span style=\"color: #000080;\"><strong>Embryonal tumor with multilayered rosettes \u00a0 ETMR (\u30b0\u30ec\u30fc\u30c9 4)<\/strong><\/span><br \/>\n\u65e7\u5206\u985e\u306e\uff0c<span style=\"color: #000080;\"><strong>ETANTR<\/strong><\/span>, CNS PNET, <strong><span style=\"color: #000080;\">\u4e0a\u8863\u82bd\u816b\u00a0ependymoblastoma, \u9ac4\u4e0a\u76ae\u816b\u00a0medulloepithelioma<\/span><\/strong>\u3092\u542b\u307f\u307e\u3059<\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/pnetembryonaltumor\/\"><strong><span style=\"color: #000080;\">\u4e2d\u67a2\u795e\u7d4c\u82bd\u816b <em>FOXR2<\/em>-activated<br \/>\n<\/span><\/strong><strong><span style=\"color: #000080;\">CNS Neuroblastoma, <em>FOXR2<\/em>-activated (\u30b0\u30ec\u30fc\u30c9 4)<\/span><\/strong><\/a><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/pnetembryonaltumor\/\"><strong><span style=\"color: #000080;\">CNS tumor with <em>BCOR<\/em> internal tandem duplication (\u30b0\u30ec\u30fc\u30c9 4)<\/span><\/strong><\/a><\/p>\n<p><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/pnetembryonaltumor\/\"><strong><span style=\"color: #000080;\">CNS embryonal tumor (\u30b0\u30ec\u30fc\u30c9 4) \u4e0a\u8a18\u306b\u7279\u5b9a\u3067\u304d\u306a\u3044\u3082\u306e<\/span><\/strong><\/a><\/p>\n<p align=\"left\">\uff08\u6ce8\uff1aPNET \u30d4\u30fc\u30cd\u30c3\u30c8\u304c\u306a\u304f\u306a\u308a\u307e\u3057\u305f\u304c\uff0c\u3053\u306e\u8a3a\u65ad\u540d\u3092\u6368\u3066\u308b\u3068\u6cbb\u7642\u65b9\u6cd5\u304c\u6587\u732e\u3067\u691c\u7d22\u3067\u304d\u307e\u305b\u3093\uff09<\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/pinealtumor\/\">\u677e\u679c\u4f53\u816b\u760d \u00a0<\/a><\/strong><\/span><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/pinealtumor\/\">Pineal tumors\u3000<\/a>\u3000<\/strong><\/span><\/h3>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/pinealtumor\/\">\u677e\u679c\u4f53\u7d30\u80de\u816b<\/a><br \/>\nPineocytoma (\u30b0\u30ec\u30fc\u30c9 1)\u3000<\/strong><\/span><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/pinealtumor\/\">\u4e2d\u9593\u578b\u677e\u679c\u4f53\u5b9f\u8cea\u816b\u760d<\/a><br \/>\nPineal parenchymal tumor of intermediate differentiation (\u30b0\u30ec\u30fc\u30c9 2, 3)\u3000<a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/pinealtumor\/\"><br \/>\n<\/a><\/span><\/strong><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/pinealtumor\/\">\u677e\u679c\u4f53\u82bd\u816b<\/a><br \/>\nPineoblastoma (\u30b0\u30ec\u30fc\u30c9 4)\u3000<\/span><\/strong><\/p>\n<p align=\"left\"><strong><span style=\"color: #000080;\"><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/pinealtumor\/\">\u677e\u679c\u4f53\u90e8\u4e73\u982d\u72b6\u816b\u760d<\/a><br \/>\nPapillary tumors of the pineal region (\u30b0\u30ec\u30fc\u30c9 2, 3)\u3000<\/span><\/strong><\/p>\n<p align=\"left\"><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/pinealtumor\/\"><span style=\"color: #000080;\"><strong>Desmoplastic myxoid tumor of the pineal region, <em>SMARKB1<\/em>-mutant<\/strong><\/span><\/a><\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong>\u8133\u795e\u7d4c\u30fb\u508d\u810a\u9ac4\u795e\u7d4c\u306e\u816b\u760d \u00a0<\/strong><\/span><span style=\"color: #000080;\"><strong>Cranial and paraspinal nerve tumors\u3000<\/strong><\/span><\/h3>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/schwann\/\">\u795e\u7d4c\u9798\u816b<\/a><br \/>\nSchwannomas (\u30b0\u30ec\u30fc\u30c9 1)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><span style=\"color: #333333;\"><a href=\"\/sawamura\/braintumors\/nf-1\/\"><strong>\u795e\u7d4c\u7dda\u7dad\u816b<\/strong><\/a><br \/>\n<span style=\"color: #000080;\"><strong>Neurofibroma (\u30b0\u30ec\u30fc\u30c9 1)<\/strong><\/span><\/span><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>Perineurioma<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>Hybrid nerve sheath tumors<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>Malignant melanotic nerve sheath tumor<\/strong><\/span><\/p>\n<p align=\"left\"><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/mpnst\/\"><strong><span style=\"color: #000080;\">\u60aa\u6027\u62b9\u6d88\u795e\u7d4c\u9798\u816b<\/span><\/strong><\/a><br \/>\n<strong><span style=\"color: #000080;\">Malignant peripheral nerve sheath tumor (MPNST)\u3000<\/span><\/strong><\/p>\n<p align=\"left\"><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/paragangliomaglomus\/\"><span style=\"color: #000080;\"><strong>\u30d1\u30e9\u30ac\u30f3\u30b0\u30ea\u30aa\u30fc\u30de\uff0c\u508d\u795e\u7d4c\u7bc0\u81a0\u816b<\/strong><\/span><\/a><br \/>\n<span style=\"color: #000080;\"><strong>Paraganglioma (grade 1)\u00a0<\/strong><\/span><\/p>\n<h3 align=\"left\"><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/meningioma\/\"><span style=\"color: #000080;\"><strong>\u9ac4\u819c\u816b \u00a0<\/strong><\/span><\/a><a href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/meningioma\/\"><span style=\"color: #000080;\"><strong>meningiomas<\/strong><\/span><\/a><\/h3>\n<p align=\"left\"><strong><span style=\"color: #000080;\">\u9ac4\u819c\u7a2e<br \/>\nMeningioma (grade 1, 2, 3)<\/span><\/strong><\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong>\u9593\u8449\u7cfb\/\u975e\u9ac4\u819c\u7d30\u80de\u816b\u760d \u00a0<\/strong><\/span><span style=\"color: #000080;\"><strong>Mesenchymal, non-meningothelial tumors \u00a0<\/strong><\/span><\/h3>\n<h5><span style=\"color: #000080;\">Soft tissure tumors: Fibroblastic and myofibroblastic tumors<\/span><\/h5>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u5b64\u5728\u7dda\u7dad\u6027\u816b\u760d SFT solitary fibrous tumor\uff0f\u8840\u7ba1\u5916\u76ae\u816b \/ hemangiopericytoma\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/solitaryfibroustumor\/\">\u5b64\u5728\u7dda\u7dad\u6027\u816b\u760d \u00a0SFT<\/a><br \/>\n<span style=\"color: #000080;\">Solitary fibrous tumor\u00a0\u00a0(SFT \u00a0\u30b0\u30ec\u30fc\u30c9 1, 2, 3)<\/span><\/strong><\/span><\/p>\n<h5><span style=\"color: #000080;\">Soft tissure tumors: Vascular tumors<\/span><\/h5>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u6d77\u7dbf\u72b6\u8840\u7ba1\u816b cavernous hemangioma, cavernous malformation, \u9759\u8108\u5947\u5f62 venous malformation\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/cavernoma\/\">\u8840\u7ba1\u816b\u3068\u8840\u7ba1\u5947\u5f62<\/a><\/strong><\/span><strong><span style=\"color: #000080;\"><br \/>\n<span style=\"caret-color: #000080;\">Hemangioma<\/span>\u00a0and vascular malformations\u00a0<\/span><\/strong><\/p>\n<p><strong><span style=\"color: #000080;\"><a style=\"color: #000080;\" title=\"\u8840\u7ba1\u82bd\u816b hemangioblastoma\uff0c\u30d5\u30a9\u30f3\u30fb\u30d2\u30c3\u30da\u30eb\u30fb\u30ea\u30f3\u30c9\u30a6\u75c5 VHL\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/hemangioblastoma\/\">\u8840\u7ba1\u82bd\u816b (\u30d5\u30a9\u30f3\u30fb\u30d2\u30c3\u30da\u30eb\u30fb\u30ea\u30f3\u30c9\u30a6\u75c5 VHL)<\/a><br \/>\n<\/span><span style=\"color: #000080;\">Hemangioblastoma (\u30b0\u30ec\u30fc\u30c9 1)<\/span><span style=\"color: #000080;\"><br \/>\n<\/span><\/strong><\/p>\n<h5><span style=\"color: #000080;\">Soft tissure tumors: Skeletal muscle tumors<\/span><\/h5>\n<p><span style=\"color: #000080;\"><strong><br \/>\n<\/strong><\/span><span style=\"color: #333333;\"><span style=\"color: #000080;\"><strong>\u6a2a\u7d0b\u7b4b\u8089\u816b<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>Rhabdomyosarcoma<\/strong> <\/span>\u00a0<\/span><\/p>\n<h5><span style=\"color: #000080;\">Soft tissure tumors: <\/span><span style=\"color: #333333;\"><span style=\"color: #000080;\">Uncertain differentiation<\/span><\/span><\/h5>\n<p><span style=\"color: #333333;\"><em><span style=\"color: #000080;\"><strong>Intracranial mesenchymal tumor, FET-CREB fusion-positive<\/strong><\/span><\/em><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong><em>CIC<\/em>-rearranged sarcoma<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>Primary intracranial sarcoma, <em>DICER1<\/em>-mutant<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>\u30e6\u30fc\u30a4\u30f3\u30b0\u8089\u816b<br \/>\nEwing Sarcoma \u00a0<\/strong><\/span><\/p>\n<h5><span style=\"color: #000080;\"><strong>Chondro-osseous tumors: Chondrogenic tumors<\/strong><\/span><\/h5>\n<p><strong><span style=\"color: #000080;\">Mesenchymal chondrosarcoma<\/span><\/strong><\/p>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u9aa8\u8edf\u9aa8\u816b\u760d osteocartilagenous tumors\" href=\"\/sawamura\/braintumors\/chondroidtumo\/\">\u8edf\u9aa8\u8089\u816b<\/a><\/strong><\/span><span style=\"color: #000080;\"><strong><br \/>\nChondrosarcoma<\/strong><\/span><\/p>\n<h5><span style=\"color: #000080;\"><strong>Chondro-osseous tumors: Notochodal tumors<\/strong><\/span><\/h5>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/chordom\/\">\u810a\u7d22\u816b<\/a><br \/>\n<\/strong><\/span><span style=\"color: #000080;\"><strong><span style=\"color: #000080;\">Chordoma <\/span><\/strong><\/span><\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong>\u30e1\u30e9\u30ce\u30b5\u30a4\u30c8\u816b\u760d \u00a0<\/strong><\/span><span style=\"color: #000080;\"><strong>Melanocytic tumors \u00a0<\/strong><\/span><\/h3>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>Diffuse meningeal melanocytic neoplasm<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong>\u00a0 \u00a0 <a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/neurocutaneous-melanosis\/\">\u9ac4\u819c\u9ed2\u8272\u816b\u75c7<\/a><br \/>\n<\/strong><\/span><span style=\"color: #000080;\"><strong>\u3000\u00a0<a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/pediattumor\/neurocutaneous-melanosis\/\">Meningeal melanocytosis and\u00a0meningeal melanomatosis\u00a0<\/a><\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>Circumscribed meningeal melanocytic neoplasms<\/strong><\/span><br \/>\n<strong><span style=\"color: #000080;\">\u00a0 \u00a0 \u9ac4\u819c\u9ed2\u8272\u816b<br \/>\n<\/span><\/strong><strong><span style=\"color: #000080;\">\u3000 Meningeal melanocytoma and meningeal melanoma\u3000<\/span><\/strong><\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong>\u30ea\u30f3\u30d1\u816b \u00a0<\/strong><\/span><span style=\"color: #000080;\"><strong>Lymphomas\u3000<\/strong><\/span><\/h3>\n<h5><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/lymphoma\/\">CNS lymphomas<\/a><\/strong><\/span><\/h5>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/lymphoma\/\">\u4e2d\u67a2\u795e\u7d4c\u539f\u767a\u5927\u7d30\u80de\u578bB\u7d30\u80de\u6027\u30ea\u30f3\u30d1\u816b <\/a><br \/>\nPrimary diffuse large B-cell lymphoma of the CNS: \u00a0<\/strong><\/span><span style=\"color: #000080;\"><strong>PCNSL<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>Immunodefficiency-associated CNS lymphoma<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/miscellaneouscnslymphoma\/\">Lymphomatoid granulomatosis \u00a0 LYG<\/a><\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>\u8840\u7ba1\u5185\u5927\u7d30\u80de\u578bB\u7d30\u80de\u6027\u30ea\u30f3\u30d1\u816b\u00a0<\/strong><\/span><br \/>\n<span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/miscellaneouscnslymphoma\/\">Intravasclar large B-cell lymphoma \u00a0 IVL<\/a><\/strong><\/span><\/p>\n<h5>Micellaneous rare lymphomas in the CNS<\/h5>\n<p><span style=\"color: #000080;\"><strong>\u786c\u819c\u30e2\u30eb\u30c8\u30ea\u30f3\u30d1\u816b<br \/>\n<span style=\"color: #000080;\"><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/miscellaneouscnslymphoma\/\">MALT lymphoma of the dura\u3000<\/a><\/span><\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>Other low-grade B-cell lymphoma of the CNS<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>Anaplastic large cell lymphoma (<em>ALK+\/ALK-<\/em>)<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>T-cell and NK\/T-cell lymphomas<\/strong><\/span><\/p>\n<h3><span style=\"color: #000080;\">Histiocytic tumors<\/span><\/h3>\n<p><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"\/sawamura\/braintumors\/langerhans\/\">\u30e9\u30f3\u30b2\u30eb\u30cf\u30f3\u30b9\u7d30\u80de\u7d44\u7e54\u75c7<\/a>\u00a0LCH<br \/>\nLangerhans cell histiiocytosis LCH<\/strong><\/span><\/p>\n<p><strong><span style=\"color: #000080;\">Erdheim-Chester disease<\/span><\/strong><\/p>\n<p><strong><span style=\"color: #000080;\">Rosai-Dorfman disease<\/span><\/strong><\/p>\n<p><strong><span style=\"color: #000080;\">Juvenile xanthogranuloma<\/span><\/strong><\/p>\n<p><strong><span style=\"color: #000080;\">Histiocytic sarcoma<\/span><\/strong><\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u80da\u7d30\u80de\u816b\u760d \u00a0<\/a><\/strong><\/span><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">Germ cell tumors<\/a><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u3000<\/a><\/strong><\/span><\/h3>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u6210\u719f\u5947\u5f62\u816b<\/a><br \/>\nMature teratoma<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u672a\u719f\u5947\u5f62\u816b<\/a><br \/>\nImmature teratoma<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u60aa\u6027\u8ee2\u5316\u3092\u4f34\u3046<\/a>\u5947\u5f62\u816b<br \/>\nTeratoma with somatic type malignancy<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u30b8\u30e3\u30fc\u30df\u30ce\u30fc\u30de\uff08\u80da\u816b\uff09\" href=\"\/sawamura\/pediattumor\/germinoma\/\">\u80da\u816b\u3000\u30b8\u30e3\u30fc\u30df\u30ce\u30fc\u30de\u00a0<\/a><br \/>\nGerminoma (\u30b0\u30ec\u30fc\u30c9 4)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u80ce\u5150\u6027\u764c<\/a><br \/>\nEmbryonal carcinoma (\u30b0\u30ec\u30fc\u30c9 4)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u5375\u9ec4\u56a2\u816b\u760d<\/a><br \/>\nYolk sac tumor (\u30b0\u30ec\u30fc\u30c9 4)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u7d68\u6bdb\u764c<\/a><br \/>\nChoriocarcinoma (\u30b0\u30ec\u30fc\u30c9 4)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u80da\u7d30\u80de\u816b\u760d\" href=\"\/sawamura\/pediattumor\/germ\/\">\u6df7\u5408\u6027\u80da\u7d30\u80de\u816b\u760d<\/a><br \/>\nMixed germ cell tumors\u3000<\/strong><\/span><\/p>\n<h3 align=\"left\"><span style=\"color: #000080;\"><strong>\u30c8\u30eb\u30b3\u978d\u90e8\u816b\u760d\u00a0<\/strong><\/span><span style=\"color: #000080;\"><strong>Tumors of the sellar region<\/strong><\/span><\/h3>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u982d\u84cb\u54bd\u982d\u816b\" href=\"\/sawamura\/braintumors\/cranio\/\">\u30a8\u30ca\u30e1\u30eb\u4e0a\u76ae\u816b\u578b\u982d\u84cb\u54bd\u982d\u816b<\/a><br \/>\nAdamantinomatous craniopharyngioma (grade 1)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u982d\u84cb\u54bd\u982d\u816b\" href=\"\/sawamura\/braintumors\/cranio\/\">\u4e73\u982d\u72b6\u982d\u84cb\u54bd\u982d\u816b<\/a><br \/>\nPapillary craniopharyngioma (grade 1)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/glioma\/%e4%b8%8b%e5%9e%82%e4%bd%93%e7%b4%b0%e8%83%9e%e8%85%ab-pituicytoma\/\">\u4e0b\u5782\u4f53\u7d30\u80de\u816b\u3002\u30c8\u30eb\u30b3\u978d\u90e8\u9846\u7c92\u7d30\u80de\u816b\uff0c\u30aa\u30f3\u30b3\u30b5\u30a4\u30c8\u30fc\u30de<br \/>\n<\/a>Pituicytoma,\u00a0Granular cell tumor of the sellar lesion, \u00a0Spindle cell oncocytoma (grade 1)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" href=\"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/pituitary\/\">\u4e0b\u5782\u4f53\u817a\u816b<br \/>\n<\/a>Pituitary adenoma\/PitNET (\u30b0\u30ec\u30fc\u30c9 1)<\/strong><\/span><\/p>\n<p align=\"left\"><span style=\"color: #000080;\"><strong>Pituitary blastoma<\/strong><\/span><\/p>\n<h3><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u8ee2\u79fb\u6027\u8133\u816b\u760d\" href=\"\/sawamura\/braintumors\/meta\/\">\u8ee2\u79fb\u6027\u8133\u816b\u760d \u00a0<\/a><\/strong><\/span><span style=\"color: #000080;\"><strong><a style=\"color: #000080;\" title=\"\u8ee2\u79fb\u6027\u8133\u816b\u760d\" href=\"\/sawamura\/braintumors\/meta\/\">Metastases to the CNS\u3000<\/a><\/strong><\/span><\/h3>\n<p><span style=\"color: #000080;\"><strong>\u8133\u810a\u9ac4\u3078\u306e\u8ee2\u79fb<br \/>\nMetastases to the brain and spinal cord\u00a0<\/strong><\/span><\/p>\n<p><span style=\"color: #000080;\"><strong>\u9ac4\u819c\u3078\u306e\u8ee2\u79fb<br \/>\nMetastases to the meninges<\/strong><\/span><\/p>\n<hr \/>\n<p>&nbsp;<\/p>\n<p style=\"text-align: center;\" align=\"left\"><img loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-1960\" title=\"tora\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2013\/01\/tora.jpg\" alt=\"\" width=\"472\" height=\"566\" \/><\/p>\n<h5 align=\"left\">2021 WHO Classification of Tumors of the Central Nervous System.<\/h5>\n<table style=\"width: 95.42375681480257%; height: 3023px;\">\n<tbody>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Gliomas, glioneuronal tumors, and neuronal tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Adult-type diffuse gliomas\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Astrocytoma, IDH-mutant\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Oligodendroglioma, IDH-mutant, and 1p\/19q-codeleted\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Glioblastoma, IDH-wildtype\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Pediatric-type diffuse low-grade gliomas\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Diffuse astrocytoma, <em>MYB<\/em>&#8211; or <em>MYBL1<\/em>-altered\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Angiocentric glioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Polymorphous low-grade neuroepithelial tumor of the young\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Diffuse low-grade glioma, MAPK pathway-altered\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Pediatric-type diffuse high-grade gliomas\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Diffuse midline glioma, H3 K27-altered\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Diffuse hemispheric glioma, H3 G34-mutant\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Diffuse pediatric-type high-grade glioma, H3-wildtype and IDH-wildtype\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Infant-type hemispheric glioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Circumscribed astrocytic gliomas\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Pilocytic astrocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003High-grade astrocytoma with piloid features\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Pleomorphic xanthoastrocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Subependymal giant cell astrocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Chordoid glioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Astroblastoma, <em>MN1<\/em>-altered\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Glioneuronal and neuronal tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Ganglioglioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Desmoplastic infantile ganglioglioma \/ desmoplastic infantile astrocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Dysembryoplastic neuroepithelial tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003<em>Diffuse glioneuronal tumor with oligodendroglioma-like features and nuclear clusters<\/em>\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Papillary glioneuronal tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Rosette-forming glioneuronal tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Myxoid glioneuronal tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Diffuse leptomeningeal glioneuronal tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Gangliocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Multinodular and vacuolating neuronal tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Dysplastic cerebellar gangliocytoma (Lhermitte-Duclos disease)\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Central neurocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Extraventricular neurocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Cerebellar liponeurocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Ependymal tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Supratentorial ependymoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Supratentorial ependymoma, <em>ZFTA<\/em> fusion-positive\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Supratentorial ependymoma, <em>YAP1<\/em> fusion-positive\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Posterior fossa ependymoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Posterior fossa ependymoma, group PFA\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Posterior fossa ependymoma, group PFB\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Spinal ependymoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Spinal ependymoma, <em>MYCN<\/em>-amplified\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Myxopapillary ependymoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Subependymoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Choroid plexus tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Choroid plexus papilloma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Atypical choroid plexus papilloma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Choroid plexus carcinoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Embryonal tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Medulloblastoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Medulloblastomas, molecularly defined\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Medulloblastoma, WNT-activated\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Medulloblastoma, SHH-activated and <em>TP53<\/em>-wildtype\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Medulloblastoma, SHH-activated and <em>TP53<\/em>-mutant\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Medulloblastoma, non-WNT\/non-SHH\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Medulloblastomas, histologically defined\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Other CNS embryonal tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Atypical teratoid\/rhabdoid tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003<em>Cribriform neuroepithelial tumor<\/em>\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Embryonal tumor with multilayered rosettes\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003CNS neuroblastoma, <em>FOXR2<\/em>-activated\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003CNS tumor with <em>BCOR<\/em> internal tandem duplication\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003CNS embryonal tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Pineal tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Pineocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Pineal parenchymal tumor of intermediate differentiation\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Pineoblastoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Papillary tumor of the pineal region\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Desmoplastic myxoid tumor of the pineal region, <em>SMARCB1<\/em>-mutant\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Cranial and paraspinal nerve tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Schwannoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Neurofibroma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Perineurioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Hybrid nerve sheath tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Malignant melanotic nerve sheath tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Malignant peripheral nerve sheath tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Paraganglioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Meningiomas\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Meningioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Mesenchymal, non-meningothelial tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Soft tissue tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Fibroblastic and myofibroblastic tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Solitary fibrous tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Vascular tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Hemangiomas and vascular malformations\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Hemangioblastoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Skeletal muscle tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Rhabdomyosarcoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Uncertain differentiation\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003<em>Intracranial mesenchymal tumor, FET-CREB fusion-positive<\/em>\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003<em>CIC<\/em>-rearranged sarcoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Primary intracranial sarcoma, <em>DICER1<\/em>-mutant\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Ewing sarcoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Chondro-osseous tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Chondrogenic tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Mesenchymal chondrosarcoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Chondrosarcoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Notochordal tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Chordoma (including poorly differentiated chordoma)\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Melanocytic tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Diffuse meningeal melanocytic neoplasms\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Meningeal melanocytosis and meningeal melanomatosis\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Circumscribed meningeal melanocytic neoplasms\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Meningeal melanocytoma and meningeal melanoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Hematolymphoid tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Lymphomas\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003CNS lymphomas\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Primary diffuse large B-cell lymphoma of the CNS\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Immunodeficiency-associated CNS lymphoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Lymphomatoid granulomatosis\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Intravascular large B-cell lymphoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Miscellaneous rare lymphomas in the CNS\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003MALT lymphoma of the dura\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Other low-grade B-cell lymphomas of the CNS\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003Anaplastic large cell lymphoma (<em>ALK<\/em>+\/<em>ALK<\/em>\u2212)\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003\u2003T-cell and NK\/T-cell lymphomas\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Histiocytic tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Erdheim-Chester disease\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Rosai-Dorfman disease\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Juvenile xanthogranuloma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Langerhans cell histiocytosis\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003\u2003Histiocytic sarcoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Germ cell tumors\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Mature teratoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 20px;\">\n<td style=\"height: 20px;\"><strong>\u2003Immature teratoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Teratoma with somatic-type malignancy\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Germinoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Embryonal carcinoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Yolk sac tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Choriocarcinoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Mixed germ cell tumor\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Tumors of the sellar region\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Adamantinomatous craniopharyngioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Papillary craniopharyngioma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Pituicytoma, granular cell tumor of the sellar region, and spindle cell oncocytoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Pituitary adenoma\/PitNET\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Pituitary blastoma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>Metastases to the CNS\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Metastases to the brain and spinal cord parenchyma\u00a0<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 21px;\">\n<td style=\"height: 21px;\"><strong>\u2003Metastases to the meninges\u00a0<\/strong><\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p align=\"left\">\n","protected":false},"excerpt":{"rendered":"<p>2021\u5e746\u6708\u306b5\u5e74\u3076\u308a\u306b\u6539\u5b9a\u3055\u308c\u307e\u3057\u305f \u591a\u304f\u306e\u816b\u760d\u578b\u3067\u907a\u4f1d\u5b50\u8a3a\u65ad\u304c\u5fc5\u8981\u3068\u306a\u308a\uff0c\u75c5\u7406\u8a3a\u65ad\u540d\u304c\u5909\u308f\u3063\u3066\u3044\u307e\u3059\u304c\uff0c\u6cbb\u7642\u65b9\u6cd5\u306e\u9032\u6b69\u306f\u8ffd\u3044\u3064\u3044\u3066\u3044\u307e\u305b\u3093\uff0c\u3067\u3059\u304b\u3089\u5f53\u9762\u6cbb\u7642\u306e\u9078\u629e\u306f2016\u5e74\u306e\u65e7\u5206\u985e\u306b\u5f93\u3063\u305f\u65b9\u304c\u3044\u3044\u3067\u3057\u3087\u3046 \u661f\u7d30\u80de [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[11,4],"tags":[],"class_list":["post-1867","post","type-post","status-publish","format-standard","hentry","category-pathocase","category-braintumors"],"aioseo_notices":[],"_links":{"self":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/1867","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/comments?post=1867"}],"version-history":[{"count":153,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/1867\/revisions"}],"predecessor-version":[{"id":1928,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/1867\/revisions\/1928"}],"wp:attachment":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/media?parent=1867"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/categories?post=1867"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/tags?post=1867"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}