{"id":10196,"date":"2017-11-05T15:00:49","date_gmt":"2017-11-05T06:00:49","guid":{"rendered":"http:\/\/plaza.umin.ac.jp\/sawamura\/?p=10196"},"modified":"2018-08-17T10:02:40","modified_gmt":"2018-08-17T01:02:40","slug":"mpnst","status":"publish","type":"post","link":"https:\/\/plaza.umin.ac.jp\/sawamura\/braintumors\/mpnst\/","title":{"rendered":"\u60aa\u6027\u672b\u68a2\u795e\u7d4c\u9798\u816b MPNST malignant peripheral nerve sheath tumor"},"content":{"rendered":"<ul>\n<li>MPNST\u3068\u547c\u3070\u308c\u307e\u3059<\/li>\n<li>\u672b\u68a2\u795e\u7d4c\u304b\u3089\u767a\u751f\u3059\u308b\u816b\u760d\u3067\u3059<\/li>\n<li>\u982d\u84cb\u5185\u306e\u3082\u306e\u306f\u6975\u3081\u3066\u7a00\u3067\uff0c\u56db\u80a2\u4f53\u5e79\u306e\u8edf\u90e8\u7d44\u7e54\u304b\u3089\u767a\u751f\u3057\u307e\u3059<\/li>\n<li>30-40\u4ee3\u306e\u4e2d\u5e74\u306b\u591a\u3044\u3067\u3059<\/li>\n<li>\u795e\u7d4c\u7dda\u7dad\u816b\u75c71\u578b <strong><span style=\"color: #000080;\">NF-1\u306b\u5408\u4f75\u3059\u308b<\/span><\/strong>\u3082\u306e\u304c50%\u3067\u3059<\/li>\n<li>\u4e2d\u3067\u3082<strong><span style=\"color: #000080;\">\u8513\u72b6\u795e\u7d4c\u9798\u816b plexiform neurofibroma\u304c\u60aa\u6027\u5316<\/span><\/strong>\u3059\u308b\u30b1\u30fc\u30b9\u304c\u591a\u3044\u3067\u3059<\/li>\n<li>NF-1\u306b\u5408\u4f75\u3059\u308b\u3082\u306e\u3067\u306f\u5e74\u9f62\u5c64\u304c20-30\u4ee3\u3067\u3059<\/li>\n<li>\u5b64\u767a\u4f8b\u3067\u306f\u5927\u304d\u306a\u672b\u68a2\u795e\u7d4c\u304b\u3089\u767a\u751f\u3059\u308b\u983b\u5ea6\u304c\u9ad8\u3044\u3067\u3059<\/li>\n<li>\u826f\u6027\u306e<span style=\"color: #000080;\"><strong>\u795e\u7d4c\u9798\u816b\u3092\u653e\u5c04\u7dda\u6cbb\u7642\u3057\u305f\u3053\u3068\u306b\u3088\u3063\u3066\u60aa\u6027\u5316<\/strong><\/span>\u3057\u3066\u751f\u3058\u305f\u3082\u306e\u304c10%\u304f\u3089\u3044\u3042\u308a\u307e\u3059\uff08\u653e\u5c04\u7dda\u8a98\u767aMPNST\uff09<\/li>\n<li>\u8133\u795e\u7d4c\u5916\u79d1\u9818\u57df\u3067\u306f\uff0c\u982d\u84cb\u5e95\u539f\u767a\u306e\u3082\u306e\u3084\uff0c\u8074\u795e\u7d4c\u816b\u760d\u306e\u653e\u5c04\u7dda\u6cbb\u7642\u5f8c\u306e\u767a\u751f\u304c\u77e5\u3089\u308c\u3066\u3044\u307e\u3059<\/li>\n<li>15%\u304f\u3089\u3044\u3067\u6bd4\u8f03\u7684\u826f\u6027\u306e\u7d4c\u904e\u3092\u3068\u308b\u3082\u306e\u304c\u3042\u308a\u307e\u3059\u304c\uff0c\u6b8b\u308a\u306f\u9ad8\u5ea6\u306e\u60aa\u6027\u816b\u760d\u3067\u3059<\/li>\n<li>5 cm\u4ee5\u4e0a\u306e\u3082\u306e\u306e\u4e88\u5f8c\u304c\u60aa\u3044\u3068\u3055\u308c\u3044\u3066\u3044\u307e\u3059<\/li>\n<\/ul>\n<hr \/>\n<p><a href=\"\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst1.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-10189\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst1-300x280.jpg\" alt=\"\" width=\"300\" height=\"280\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst1-300x280.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst1-550x514.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst1.jpg 709w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><a href=\"\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst2.jpg\"><img loading=\"lazy\" decoding=\"async\" class=\"alignleft size-medium wp-image-10190\" src=\"\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst2-300x285.jpg\" alt=\"\" width=\"300\" height=\"285\" srcset=\"https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst2-300x285.jpg 300w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst2-550x523.jpg 550w, https:\/\/plaza.umin.ac.jp\/sawamura\/wp\/wp-content\/uploads\/2012\/04\/mpnst2.jpg 709w\" sizes=\"auto, (max-width: 300px) 100vw, 300px\" \/><\/a><\/p>\n<p>\u53f3\u306f\u304c\u30c9\u30ea\u30cb\u30a6\u30e0\u5897\u5f37MRI\u3067\u3059\u3002NF-1\u60a3\u8005\u3055\u3093\u306e\u53f3\u6df1\u9838\u90e8\u306eplexiform neurofibroma\u306b\u767a\u751f\u3057\u305f\u3082\u306e\u3067\u3059\u3002\u901a\u5e38\u306e\u795e\u7d4c\u9798\u816b\u306b\u6bd4\u8f03\u3057\u3066\u5883\u754c\u304c\u4e0d\u9bae\u660e\u3067\u5897\u5927\u901f\u5ea6\u304c\u65e9\u3044\u3053\u3068\u304c\u7279\u5fb4\u3067\u3059\u3002<\/p>\n<h5>\u8a3a\u65ad<\/h5>\n<ul>\n<li>MRI\u3067\u306f\u5883\u754c\u4e0d\u9bae\u660e\u306a\u4e0d\u898f\u5247\u306b\u5897\u5f37\u3055\u308c\u308b\u816b\u760d\u3067\u3059<\/li>\n<li>FDG-PET\u3067\u9ad8\u3044\u53d6\u308a\u8fbc\u307f up-take\u304c\u8a8d\u3081\u3089\u308c\u307e\u3059<\/li>\n<\/ul>\n<h5>\u75c5\u7406<\/h5>\n<p>neurofibroma\/schwannoma\u3067\uff0c\u5178\u578b\u7684\u306a\u7d30\u80de\u914d\u5217\u304c\u5931\u308f\u308c\uff0c\u7d30\u80de\u5bc6\u5ea6\u304c\u304b\u306a\u308a\u9ad8\u3044\uff0c\u304b\u3064\u7d30\u80de\u7570\u578b\u6027\u304c\u3042\u308b\u3068<strong><span style=\"color: #000080;\">ANF<\/span><\/strong> atypical neurofibroma\u3068\u547c\u3070\u308c\u307e\u3059\uff0c\u5358\u795e\u7d4c\u306e\u795e\u7d4c\u9798\u816b\u3042\u308b\u3044\u306fplexiform neurofibroma\u304catypical neurofibroma\u3068\u306a\u308a\uff0c\u3055\u3089\u306bMPNST\u3078\u3068\u60aa\u6027\u5316\u3059\u308b\u6240\u898b\u304c\u77e5\u3089\u308c\u3066\u3044\u307e\u3059<\/p>\n<h5>\u6cbb\u7642<\/h5>\n<ul>\n<li>\u6cbb\u3059\u65b9\u6cd5\u306f\u624b\u8853\u306b\u3088\u308b\u5b8c\u5168\u6458\u51fa\u3067\u3059<\/li>\n<li>\u3057\u304b\u3057\uff0c\u5468\u56f2\u7d44\u7e54\u306b\u6d78\u6f64\u3057\u3066\u3044\u3066\u53d6\u304d\u308c\u306a\u3044\u3053\u3068\u304c\u591a\u3044\u3067\u3059<\/li>\n<li>\u982d\u76ae\u306a\u3069\u6d45\u3044\u90e8\u5206\u304b\u3089\u8868\u9762\u306b\u76db\u308a\u4e0a\u304c\u3063\u3066\u3044\u308b\u3082\u306e\u306f\u5168\u6458\u51fa\u3067\u304d\u3066\u6cbb\u308b\u3053\u3068\u304c\u3042\u308a\u307e\u3059<\/li>\n<li>\u653e\u5c04\u7dda\u6cbb\u7642\u3067\u5c40\u6240\u5236\u5fa1\u304c\u3067\u304d\u308b\u3053\u3068\u304c\u3042\u308a\u307e\u3059<\/li>\n<li>\u3067\u3082\u591a\u304f\u306f\uff0c\u901a\u5e38\u306e\u653e\u5c04\u7dda\u6cbb\u7642\u306b\u306f\u62b5\u6297\u6027\u3067\u3059<\/li>\n<li>\u9ad8\u7dda\u91cf\u306e\u653e\u5c04\u7dda\u5916\u79d1\u6cbb\u7642\u304c\u6709\u52b9\u306a\u3053\u3068\u304c\u3042\u308a\u307e\u3059<\/li>\n<li>\u5316\u5b66\u7642\u6cd5\u3067\u6709\u52b9\u306a\u3082\u306e\u306f\u77e5\u3089\u308c\u3066\u3044\u307e\u305b\u3093<\/li>\n<\/ul>\n<h5>\u624b\u8853<\/h5>\n<ul>\n<li>\u5927\u304d\u306a\u3082\u306e\u3067\u306f\u5168\u6458\u51fa\u3059\u308b\u3053\u3068\u306f\u4e0d\u53ef\u80fd\u3067\u3059<\/li>\n<li>\u7d30\u3044\u795e\u7d4c\u306e\u5206\u679d\u306b\u6cbf\u3063\u3066\u5468\u56f2\u306b\u975e\u5e38\u306b\u5e83\u7bc4\u56f2\u306b\u5e83\u304c\u3063\u3066\u3044\u307e\u3059<\/li>\n<li>\u5468\u56f2\u8edf\u90e8\u7d44\u7e54\uff0c\u795e\u7d4c\u7d44\u7e54\u3092\u5dfb\u304d\u8fbc\u3093\u3067\u6d78\u6f64\u3057\u3066\u3044\u307e\u3059\u306e\u3067\uff0c\u5265\u96e2\u64cd\u4f5c\u3067\u6458\u51fa\u3059\u308b\u3053\u3068\u304c\u3067\u304d\u307e\u305b\u3093<\/li>\n<li>\u51fa\u8840\u6027\u3067\u6975\u3081\u3066\u786c\u3044\u816b\u760d\u3067\u3059<\/li>\n<\/ul>\n<h5>\u4e88\u5f8c<\/h5>\n<ul>\n<li>\u80ba\u306a\u3069\u3078\u5168\u8eab\u8ee2\u79fb\u3059\u308b\u3053\u3068\u304c25%\u304f\u3089\u3044\u3042\u308a\u307e\u3059<\/li>\n<li>\u982d\u84cb\u5185\u306e\u3082\u306e\u306f\u9ac4\u6db2\u64ad\u7a2e\u3059\u308b\u3053\u3068\u304c\u3042\u308a\u307e\u3059<\/li>\n<\/ul>\n<h5>\u75c5\u7406<\/h5>\n<ul>\n<li>\u5358\u7d14\u306aspindle cell\u304b\u3089\u306a\u308b\u3082\u306e\u3084\u9ad8\u5ea6\u306e\u591a\u578b\u6027\u3092\u793a\u3059\u3082\u306e\u307e\u3067\u3042\u308a\u307e\u3059<\/li>\n<\/ul>\n<h5>\u8cac\u4efb\u907a\u4f1d\u5b50<\/h5>\n<ul>\n<li><em>NF-1, CDKN-2A, PRC2<\/em>\u907a\u4f1d\u5b50\u306e\u76f8\u4e92\u4f5c\u7528\u3067\u767a\u751f\u3059\u308b\u3068\u8003\u3048\u3089\u308c\u3066\u3044\u307e\u3059<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>MPNST\u3068\u547c\u3070\u308c\u307e\u3059 \u672b\u68a2\u795e\u7d4c\u304b\u3089\u767a\u751f\u3059\u308b\u816b\u760d\u3067\u3059 \u982d\u84cb\u5185\u306e\u3082\u306e\u306f\u6975\u3081\u3066\u7a00\u3067\uff0c\u56db\u80a2\u4f53\u5e79\u306e\u8edf\u90e8\u7d44\u7e54\u304b\u3089\u767a\u751f\u3057\u307e\u3059 30-40\u4ee3\u306e\u4e2d\u5e74\u306b\u591a\u3044\u3067\u3059 \u795e\u7d4c\u7dda\u7dad\u816b\u75c71\u578b NF-1\u306b\u5408\u4f75\u3059\u308b\u3082\u306e\u304c50%\u3067\u3059 \u4e2d\u3067\u3082\u8513\u72b6\u795e\u7d4c\u9798\u816b p [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[4],"tags":[],"class_list":["post-10196","post","type-post","status-publish","format-standard","hentry","category-braintumors"],"aioseo_notices":[],"_links":{"self":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/10196","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/comments?post=10196"}],"version-history":[{"count":8,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/10196\/revisions"}],"predecessor-version":[{"id":11338,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/posts\/10196\/revisions\/11338"}],"wp:attachment":[{"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/media?parent=10196"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/categories?post=10196"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/plaza.umin.ac.jp\/sawamura\/wp-json\/wp\/v2\/tags?post=10196"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}